FERRO, S. Mão de et al. Segmental Caroli's Disease in a 73 years male. []. , 14, 1, pp.22-25. ISSN 0872-8178.

Case Report: A 73 year old male was admitted with cholangitis. Abdominal ultrasound and magnetic resonance cholangiopancreatography showed sacular dilation and stones in the left intrahepatic biliary tree, compatible with segmental Caroli's disease. He was treated with Imipenem. Four days after discharge he was readmitted with cholangitis and underwent a ERCP with sphincterotomy and removal of the stones. Due to recurrence of the symptoms a left hepatectomy was performed. Comments: Caroli's disease is a congenital condition, frequently asymptomatic before age 20 years or more rarely throughout the entire lifespan. It is characterised by intrahepatic ductal dilations. Segmental involvement is present in 20% of cases. Intraductal stones and cholangitis are frequent complications. Surgery is the treatment of choice for segmental disease.

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