Pênfigo Vulgar com Envolvimento Anal

 

Ana Margarida Vieira, Cláudia Cardoso, Élia Gamito, Ana Luísa Alves, Ana Paula Oliveira

Serviço de Gastrenterologia, Centro Hospitalar de Setúbal - Hospital de São Bernardo, EPE

Correspondência

 

RESUMO

INTRODUÇÃO: O envolvimento anal em doentes com Pênfigo Vulgar tem sido raramente reportado. Apresentamos o caso de uma doente de 76 anos com diagnóstico de Pênfigo Vulgar muco-cutâneo, sob corticoterapia sistémica, que inicia quadro proctológico caracterizado por hematoquézias e proctalgia associado a obstipação e dificuldade defecatória. A rectosigmoidoscopia flexível não mostrou alterações, mas o exame proctológico revelou coroa de mariscas com múltiplas erosões, compatível com Pênfigo Vulgar anal. Após corticoterapia local e normalização do trânsito intestinal, verificou-se cicatrização das lesões anais.

PALAVRAS-CHAVE: Pênfigo vulgar, pênfigo vulgar anal, envolvimento gastrointestinal no pênfigo vulgar.

 

Pemphigus Vulgaris with Anal Involvement

ABSTRACT

INTRODUCTION: Anal involvement in patients with Pemphigus Vulgaris has rarely been reported. We report a case of a 76-year-old woman with muco-cutaneous Pemphigus Vulgaris on systemic corticotherapy who started with hematochezia and anal pain associated with constipation and difficult defecation. Flexible sigmoidoscopy was normal but proctologic examination revealed skin tags with multiple erosions. After local corticotherapy and normalization of bowel movements, healing of anal lesions was seen.

KEY-WORDS: Pemphigus vulgaris, anal pemphigus vulgaris, gastrointestinal involvment in pemphigus.

 

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Correspondência: Ana Margarida Duarte da Silva Vieira; Telemóvel: +351 961 704 152; Email: ana.amdsv@gmail.com.

 

Recebido para publicação: 29/09/2009 e Aceite para publicação: 24/09/2010.