Sequestro broncopulmonar – Experiência de 12 anos

 

Bronchopulmonary sequestration – A 12-year experience

 

 

Julieta Vieira ¹

Ana Rego ¹

Ana Oliveira ¹

Daniela Sá Ferreira ¹

Antónia Furtado ²

António Couceiro ³

José António Miranda ⁴

Francisco Leal ⁵

Luís Vouga ⁶

 

 

Resumo

Sequestro broncopulmonar (SBP), também denominado sequestro pulmonar, define-se como uma malformação congénita do tracto respiratório inferior, consistindo numa porção de tecido pulmonar que não está em normal comunicação com a árvore traqueobrônquica e que recebe suprimento sanguíneo arterial através da circulação sistémica. Pode classificar-se em sequestro intralobar (SIL) e sequestro extralobar (SEL), dependendo da sua relação com o restante parênquima pulmonar. O SIL é a forma mais comum, correspondendo a cerca de 75% dos sequestros pulmonares. Os autores descrevem uma série de 8 casos, com diagnóstico anatomopatológico compatível com SBP após cirurgia, no período entre 1994 e 2005. A lobectomia foi o procedimento predominante. Os resultados após tratamento cirúrgico foram excelentes, com morbilidade mínima.

Palavras-chave: Sequestro broncopulmonar, diagnóstico, tratamento, cirurgia.

 

Abstract

Bronchopulmonary sequestration (BPS) is a rare malformation of the lower respiratory tract. It consists of a non-functioning mass of lung tissue that lacks normal communication with the tracheobronchial tree and that receives arterial blood supply from the systemic circulation. It is classified as intralobar (ILS) or extralobar (ELS) according to its location within or outside the normal lung. Most sequestrations are intralobar (75%) and occur predominantely in the left lower lobe. The authors describe a series of 8 cases of BPS in the period between 1994 and 2005, with diagnosis by histologic examination after surgery. Lobectomy was the predominant procedure. The results after surgical treatment were excellent with minimal morbidity.

Key-words: Bronchopulmonary sequestration, diagnosis, treatment, surgery.

 

 

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¹ Interna Complementar de Pneumologia do Centro Hospitalar de Vila Nova de Gaia (CHVNG)/ Complementary Pulmonology Intern, Centro Hospitalar de Vila Nova de Gaia (CHVNG)

² Interna Complementar de Anatomia Patológica do CHVNG/ Complementary Pathology Intern, CHVNG

³ Director do Serviço de Anatomia Patológica do CHVNG/ Director, Pathology Unit, CHVNG

⁴ Assistente Hospitalar de Cirurgia Cardiotorácica do CHVNG/ Hospital Assistant, Cardiothoracic Surgery, CHVNG

⁵ Assistente Graduado Hospitalar de Cirurgia Cardiotorácica do CHVNG/ Graduate Hospital Assistant, Cardiothoracic Surgery, CHVNG

⁶ Director do Serviço de Cirurgia Cardiotorácica do CHVNG/ Director, Cardiothoracic Surgery Unit, CHVNG

 

Serviço de Pneumologia do CHVNG – Director: Dr. Raul César Sá/ Pulmonology Unit, CHVNG – Director: Dr. Raul César Sá

Serviço de Cirurgia Cardiotorácica do CHVNG – Director: Dr. Luís Vouga/ Cardiothoracic Surgery Unit, CHVNG –Director: Dr. Luís Vouga

Serviço de Anatomia Patológica do CHVNG – Director: Dr. António Couceiro/ Pathology Unit, CHVNG – Director: Dr. António Couceiro

 

Recebido para publicação/received for publication: 06.03.29

Aceite para publicação/accepted for publication: 06.06.09