Abstract

MOURA, M. Carneiro de; NUNES, P. Sampaio; FLORES, H.  and  LEMOS, P. Sande. Hemangioendotelioma Hepático Infantil e Rim Displásico Multiquístico: uma nova associação?. J Port Gastrenterol. [online]. 2009, vol.16, n.2, pp.68-71. ISSN 0872-8178.

Infantile hemangioendothelioma has an incidence that is the third most common between hepatic tumours in children and the most common benign vascular tumour of the liver in infancy. In this paper we report a clinical case of a child with hepatic hemangioendothelioma associated with a transitory multicystic dysplastic kidney. The multicystic disorder was evident pre and post natally. At 5 months an ultrasonography imaging showed multiple hepatic lesions suggestive of hemangioendothelioma. At 8 months a magnetic resonance imaging did not show the right kidney. Hepatic biopsy confirmed the diagnosis of infantile hemangioendothelioma. On ultrasonographies performed during follow up focal hepatic lesions reduced and disappeared by 19 months. This association has not been reported although cases associated with unilateral renal agenesis are known.

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