Abstract

FERREIRA, M. et al. Síndrome de Klippel-trenaunay: relato de um caso com envolvimento digestivo e revisão da literatura. J Port Gastrenterol. [online]. 2009, vol.16, n.4, pp.163-167. ISSN 0872-8178.

Vascular anomalies are a common cause of gastrointestinal hemorrhage; they can occur separately or as part of a syndrome. The authors describe the clinical case of a patient with the Klippel- Trenaunay syndrome (SKT), a rare, congenital vascular anomaly, of unknown etiology, characterized by the clinical triad of cutaneous hemangiomas, varicosities and hypertrophy of soft tissue and bones, usually affecting one extremity. Gastrointestinal involvement is rare; digestive hemorrhage is the most frequent symptom, as a result of colonic vascular malformations. The authors provide a literature review concerning the most relevant aspects of diagnosis and treatment of the gastrointestinal complications of this syndrome.

Keywords : Vascular malformations; Digestive bleeding; Klippel-Trénaunaysíndrome.

        · abstract in Portuguese     · text in Portuguese     · Portuguese ( pdf )