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Revista Portuguesa de Pneumologia

versión impresa ISSN 0873-2159

Resumen

LOPES, Alexandra  y  BARATA, Fernando. About a case of common variable immunodeficiency: Revision of hypogammaglobulinemias. Rev Port Pneumol [online]. 2006, vol.12, n.3, pp.293-301. ISSN 0873-2159.

Common variable immunodeficiency is a primary immune deficiency characterized by heterogeneous immunologic disorders of unknown etiology. Its clinical manifestations include recurrent infections, autoimmune diseases, lymphoid hyperplasia, granulomatous diseases and malignancy. It can appear in patients with immunoglobulin A deficiency. The authors report the clinical case of a patient with common variable immunodeficiency and history of respiratory infections from the age of 9 months old, associated with the appearing of bronchiectasis.

Palabras clave : Common variable immunodeficiency.

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