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Revista Portuguesa de Pneumologia

versión impresa ISSN 0873-2159

Resumen

SALEIRO, Sandra; HESPANHOL, Venceslau Pinto  y  MAGALHAES, Adriana. Primary tracheobronchial amyloidosis: Two case reports. Rev Port Pneumol [online]. 2008, vol.14, n.4, pp.541-544. ISSN 0873-2159.

Primary tracheobronchial amyloidosis is a form of respiratory amyloidosis, characterised by insoluble amyloid fibril proteins deposits along the airways wall. It is an uncommon disease, requiring a tissue sample to establish the definite diagnosis based on specific pathological features. The authors report two cases of tracheobronchial amyloidosis, describing their symptoms and the diagnostic and therapeutic procedures that were performed.

Palabras clave : Amyloidosis; tracheobronchial.

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