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Revista Portuguesa de Pneumologia
Print version ISSN 0873-2159
Abstract
BENTO, Alexandra and GONCALVES, Ana Paula. Spontaneous hemothorax in a neurofibromatosis type I patient: A case report. Rev Port Pneumol [online]. 2009, vol.15, n.5, pp.937-941. ISSN 0873-2159.
Spontaneous hemothorax is a rare and potentially lethal neurofibromatosis complication. Several pathological mechanisms may explain the associated vasculopathy: a) direct vascular invasion from adjacent tumors such as Shwannoma, neurofibroma or neurofibrosarcoma; b) vascular dysplasia with stenotic or aneurysm formation6,7,9. Other mechanisms involved may include pleuropulmonar pathologies (necrotizing infections, pulmonary embolism, endometriosis, neoplasms) and blood dyscrasias. The authors describe a case of a 33 years old female, who went to the ER Service complaining with right persistent hemithora cic pain, extending to the ipsilateral shoulder and shoulder blade, without aggravation or relieving factors, since the last 8 days.
Keywords : Neurofibromatosis; spontaneous hemothorax.