Abstract

FREIRE1, Gonçalo et al. Rectal Peripheral Primitive Neuroectodermal Tumor: Case Report and Radio-Pathological Correlation. Acta Radiol Port [online]. 2020, vol.32, n.1, pp.19-21.  Epub June 04, 2021. ISSN 2183-1351.  https://doi.org/10.25748/arp.18113.

Only a few cases of peripheral Primary Neuroectodermal Tumor (pPNET) arising in the rectum have been described in the literature. We report a case of a 54-year- old male patient with urinary retention and lower abdominal pain, whose CT and MRI demonstrated a pelvic mass compressing the rectum and bladder. After surgical resection, histologic and immunohistochemical findings were compatible with a rectal pPNET, with a proliferation index of 10%. This case draws the attention to a rare and aggressive condition that has no specific symptoms or typical imaging features, consisting of a rapid growing tumor with poor prognosis, even after surgical resection and chemotherapy.

Keywords : Peripheral primitive neuroectodermal tumor; Computed tomography; Magnetic resonance imaging..

        · abstract in Portuguese     · text in English     · English ( pdf )