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Acta Radiológica Portuguesa

versión impresa ISSN 2183-1351

Resumen

SAMOUCO, Lúcia; MAGALHAES, Maria João  y  AFONSO, Mariana. Retroperitoneal Extra-Adrenal Myelolipoma: A Diagnostic Challenge with Pathological Correlation. Acta Radiol Port [online]. 2023, vol.35, n.2, pp.36-39.  Epub 31-Ago-2023. ISSN 2183-1351.  https://doi.org/10.25748/arp.28932.

Myelolipomas are benign tumors composed of adipocytes and hematopoietic cells, presenting in older adults. They commonly occur in the adrenal gland and less frequently in extra-adrenal locations. Their etiology is unknown, but eventually related to adrenocorticotropic hormonal excess. Most extra-adrenal myelolipomas are detected incidentally on cross-sectional imaging, they have mature fat and radiologically are difficult to differentiate from other neoplasm with fat, including liposarcoma.

We present a case of an extra-adrenal myelolipoma in a perirenal location and discuss its epidemiology, pathologic and radiologic features, differential diagnosis, and management.

Palabras clave : Myelolipoma; Extra-adrenal myelolipoma; Retroperitoneal neoplasms; Diagnostic imaging..

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