<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0872-0754</journal-id>
<journal-title><![CDATA[Nascer e Crescer]]></journal-title>
<abbrev-journal-title><![CDATA[Nascer e Crescer]]></abbrev-journal-title>
<issn>0872-0754</issn>
<publisher>
<publisher-name><![CDATA[Centro Hospitalar do Porto]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0872-07542020000400200</article-id>
<article-id pub-id-type="doi">10.25753/birthgrowthmj.v29.i4.18079</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[CONGENITAL PULMONARY AIRWAY MALFORMATION AND BRONCHOPULMONARY SEQUESTRATION IN INFANTS - A RARE DIAGNOSIS]]></article-title>
<article-title xml:lang="pt"><![CDATA[MALFORMAÇÃO CONGÉNITA DAS VIAS AÉREAS PULMONARES E SEQUESTRO PULMONAR NO LACTENTE - UM DIAGNÓSTICO RARO]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cachão]]></surname>
<given-names><![CDATA[Joana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Raminhos]]></surname>
<given-names><![CDATA[Isabel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Martins]]></surname>
<given-names><![CDATA[José D.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Bravio]]></surname>
<given-names><![CDATA[Ivan]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Centro Hospitalar de Setúbal Hospital de São Bernardo Department of Pediatrics]]></institution>
<addr-line><![CDATA[Setúbal ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Centro Hospitalar de Lisboa Central Hospital de Santa Marta Department of Pediatrics Cardiology]]></institution>
<addr-line><![CDATA[Lisboa ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Centro Hospitalar de Lisboa Central Hospital de Santa Marta Department of Cardiothoracic Surgery]]></institution>
<addr-line><![CDATA[Lisboa ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<volume>29</volume>
<numero>4</numero>
<fpage>200</fpage>
<lpage>203</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S0872-07542020000400200&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S0872-07542020000400200&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S0872-07542020000400200&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Congenital pulmonary airway malformation and bronchopulmonary sequestration are rare congenital anomalies. Herein is described the case of a two-month-old female infant with recurrent respiratory infections, admitted to the Pediatric Emergency Department with productive cough, respiratory distress, and fever. Chest radiography showed an heterogenous hypotransparent image in the left pulmonary field and contralateral deviation of the mediastinum. Angiotomography revealed bilateral bronchopulmonary sequestration and a systemic vessel contributing to area irrigation. The patient was submitted to vessel occlusion and lacquering, left inferior lobectomy, and resection of a right lower lobe segment. Histological examination confirmed intralobar bronchopulmonary sequestration and type 2 congenital pulmonary airway malformation in the left lung, and extralobar bronchopulmonary sequestration in the right lung. With this report, the authors intend to emphasize the importance of clinical suspicion of congenital anomalies in infants with recurrent respiratory infections.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo A malformação congénita das vias aéreas pulmonares e o sequestro pulmonar são anomalias congénitas raras. É apresentado o caso de uma lactente de dois meses com infeções respiratórias de repetição, que recorreu à Urgência Pediátrica hospitalar por tosse produtiva, dificuldade respiratória e febre. A radiografia torácica evidenciou uma imagem hipotransparente heterogénea no campo pulmonar esquerdo e desvio contralateral do mediastino e a angiotomografia revelou sequestro pulmonar bilateral e presença de vaso sistémico a irrigar a área. A doente foi submetida a oclusão e laqueação do vaso, lobectomia inferior esquerda e resseção de segmento do lobo inferior direito. O exame histológico confirmou sequestro pulmonar intralobar associado a malformação congénita das vias aéreas pulmonares tipo 2 à esquerda e sequestro pulmonar extralobar à direita. Com este caso, os autores pretendem salientar a importância da suspeição clínica de anomalias congénitas perante um lactente com infeções respiratórias de repetição.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[bronchopulmonary sequestration]]></kwd>
<kwd lng="en"><![CDATA[congenital cystic adenomatoid malformation]]></kwd>
<kwd lng="en"><![CDATA[infant]]></kwd>
<kwd lng="pt"><![CDATA[lactente]]></kwd>
<kwd lng="pt"><![CDATA[malformação adenomatóide quística congénita]]></kwd>
<kwd lng="pt"><![CDATA[sequestro pulmonary]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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