<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0872-0754</journal-id>
<journal-title><![CDATA[Nascer e Crescer]]></journal-title>
<abbrev-journal-title><![CDATA[Nascer e Crescer]]></abbrev-journal-title>
<issn>0872-0754</issn>
<publisher>
<publisher-name><![CDATA[Centro Hospitalar do Porto]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0872-07542021000100064</article-id>
<article-id pub-id-type="doi">10.25753/birthgrowthmj.v30.i1.18956</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Imaging clinical case]]></article-title>
<article-title xml:lang="pt"><![CDATA[Caso clínico imagiológico]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cristina]]></surname>
<given-names><![CDATA[Catarina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Serras]]></surname>
<given-names><![CDATA[Inês]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Santos]]></surname>
<given-names><![CDATA[Ema]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Alves]]></surname>
<given-names><![CDATA[Rui]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Serrano]]></surname>
<given-names><![CDATA[Dulce]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Centro Hospitalar Universitário do Algarve Unidade de Portimão Department of Pediatrics]]></institution>
<addr-line><![CDATA[Portimão ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Centro Hospitalar Universitário de Lisboa Central Hospital Dona Estefânia Department of Pediatrics Surgery]]></institution>
<addr-line><![CDATA[Lisboa ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2021</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2021</year>
</pub-date>
<volume>30</volume>
<numero>1</numero>
<fpage>64</fpage>
<lpage>66</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S0872-07542021000100064&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S0872-07542021000100064&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S0872-07542021000100064&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Hirschsprung disease is the most common congenital gut motility disorder and usually diagnosed in the neonatal period. It is caused by an aganglionic bowel segment resulting in absence of intestinal peristalsis and functional obstruction. Diagnosis should be considered in all patients with constipation that does not respond to conventional treatment. Radiography and contrast enema are important diagnostic exams, but the definitive diagnosis is established through histochemical analysis of aganglionic segment biopsy. Treatment is surgical and early recognition is important to avoid complications and improve prognosis. Herein is reported the clinical case of a young infant presenting to the Pediatric Emergency Department with nausea, vomiting, constipation, refusal to feed, and important abdominal distension. Abdominal radiograph and contrast enema were compatible with Hirschsprung disease. Biopsy histochemical analysis confirmed the diagnosis and surgical treatment was performed.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo A doença de Hirschsprung é o distúrbio congénito de motilidade intestinal mais comum e habitualmente diagnosticado no período neonatal. É causado por um segmento intestinal aganglionar, que leva a ausência de peristaltismo intestinal e obstrução funcional. O diagnóstico deve ser considerado em todos os doentes com obstipação sem resposta ao tratamento convencional. A radiografia e o enema com contraste são exames importantes para o diagnóstico, mas este só é definitivamente estabelecido por análise histoquímica da biópsia do segmento aganglionar. O tratamento é cirúrgico e o reconhecimento precoce da doença é importante para evitar complicações e melhorar o prognóstico. É reportado o caso clínico de um lactente que se apresentou no Serviço de Urgência Pediátrica com náuseas, vómitos, obstipação, recusa alimentar e uma importante distensão abdominal. A radiografia abdominal e o enema com contraste foram compatíveis com doença de Hirschsprung. A análise histoquímica da biópsia confirmou o diagnóstico e foi efetuado tratamento cirúrgico.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[contrast enema]]></kwd>
<kwd lng="en"><![CDATA[Hirschsprung disease]]></kwd>
<kwd lng="en"><![CDATA[intestinal obstruction]]></kwd>
<kwd lng="en"><![CDATA[meconium]]></kwd>
<kwd lng="pt"><![CDATA[clister opaco]]></kwd>
<kwd lng="pt"><![CDATA[doença de Hirschsprung]]></kwd>
<kwd lng="pt"><![CDATA[mecónio]]></kwd>
<kwd lng="pt"><![CDATA[obstrução intestinal]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="book">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Nunes]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
</person-group>
<source><![CDATA[Doença de Hirschsprung]]></source>
<year>2015</year>
<publisher-name><![CDATA[Faculdade de Medicina de Lisboa]]></publisher-name>
</nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Langer]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Hirchsprung Disease]]></article-title>
<source><![CDATA[Curr Opin Pediatr]]></source>
<year>2013</year>
<volume>25</volume>
<page-range>368-74</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Wetherill]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Sutcliffe]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Hirchsprung Disease and anorectal malformation]]></article-title>
<source><![CDATA[Early Human Development]]></source>
<year>2014</year>
<volume>90</volume>
<page-range>927-32</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Romaneli]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Ribeiro]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Bustorff-Silva]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Carvalho]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Lomazi]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Hirchsprung disease - Postsurgical intestinal dysmotality]]></article-title>
<source><![CDATA[Rev Paul Pediatr]]></source>
<year>2016</year>
<volume>34</volume>
<page-range>388-92</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Wesson]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Lopez]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Congenital aganglionic megacolon (Hirchsprung Disease)]]></article-title>
<source><![CDATA[UptoDate]]></source>
<year>2018</year>
</nlm-citation>
</ref>
</ref-list>
</back>
</article>
