<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0872-0754</journal-id>
<journal-title><![CDATA[Nascer e Crescer]]></journal-title>
<abbrev-journal-title><![CDATA[Nascer e Crescer]]></abbrev-journal-title>
<issn>0872-0754</issn>
<publisher>
<publisher-name><![CDATA[Centro Hospitalar do Porto]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0872-07542021000200109</article-id>
<article-id pub-id-type="doi">10.25753/birthgrowthmj.v30.i2.19077</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Kawasaki disease in a five-month-old infant]]></article-title>
<article-title xml:lang="pt"><![CDATA[Doença de Kawasaki num recém-nascido de cinco meses]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Maciel]]></surname>
<given-names><![CDATA[Juliana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Meireles]]></surname>
<given-names><![CDATA[Daniel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Magalhães]]></surname>
<given-names><![CDATA[Mariana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Gonçalves]]></surname>
<given-names><![CDATA[Sara]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Fernandes]]></surname>
<given-names><![CDATA[Sofia Ribeiro]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Fernandes]]></surname>
<given-names><![CDATA[Paula Cristina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Centro Hospitalar de Leiria Hospital de Santo André Department of Pediatrics]]></institution>
<addr-line><![CDATA[Leiria ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Centro Hospitalar Universitário do Porto Centro Materno-Infantil do Norte Department of Pediatrics]]></institution>
<addr-line><![CDATA[Porto ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Centro Hospitalar Universitário do Porto Centro Materno-Infantil do Norte Department of Pediatric Cardiology]]></institution>
<addr-line><![CDATA[Porto ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Centro Hospitalar Universitário do Porto Centro Materno-Infantil do Norte Department of Pediatrics Intensive Care]]></institution>
<addr-line><![CDATA[Porto ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>30</day>
<month>06</month>
<year>2021</year>
</pub-date>
<pub-date pub-type="epub">
<day>30</day>
<month>06</month>
<year>2021</year>
</pub-date>
<volume>30</volume>
<numero>2</numero>
<fpage>109</fpage>
<lpage>113</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S0872-07542021000200109&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S0872-07542021000200109&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S0872-07542021000200109&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Introduction:  Kawasaki disease, an acute self-limited vasculitis of small and medium arteries of unknown etiology, is the leading cause of heart disease in children in most developed countries. If untreated, it can lead to coronary artery dilatation and aneurysm, placing patients at risk for coronary thrombosis, myocardial infarction, or sudden death.  Case Report:  A previously healthy five-month-old boy presented with a history of respiratory symptoms and fever, being admitted for respiratory syncytial virus bronchiolitis. He maintained fever for five days associated with progressive clinical worsening and sequential development of conjunctival injection, cracked lips, swelling of hands and feet, and polymorphous rash of the limbs. Diagnostic procedures showed increased levels of inflammatory markers, hyponatremia, hypoalbuminemia, sterile pyuria, and aseptic meningitis. Despite an initial normal echocardiogram, Kawasaki disease was suspected and the boy started intravenous immunoglobulin on the fifth day. On the seventh day, echocardiogram showed signs of pancarditis and mild coronary artery ectasia and acetylsalicylic acid was started. The boy was discharged, but eight days later echocardiogram revealed major and diffuse coronary artery ectasia in a follow-up consultation and he was readmitted to start corticosteroid therapy. After five months, the boy displayed normalization of cardiac changes, without further complications.  Comments:  Kawasaki disease below six months of age is rare and associated with a high risk of coronary artery aneurysm. It is important to recognize the clinical and laboratory criteria associated with this entity and start early treatment, avoiding cardiac complications.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo  Introdução:  A doença de Kawasaki, uma vasculite aguda e autolimitada das artérias de pequeno e médio calibre de etiologia desconhecida, é a principal causa de doença cardíaca em idade pediátrica nos países desenvolvidos. Em ausência de tratamento, pode levar a ectasia e aneurisma das artérias coronárias, colocando os doentes em risco de trombose coronária, enfarte agudo do miocárdio e morte súbita.  Caso Clínico:  Um lactente de cinco meses do sexo masculino, previamente saudável, foi internado com diagnóstico de bronquiolite aguda a vírus sincicial respiratório. Manteve febre e agravamento do estado geral durante cinco dias, associado ao aparecimento sequencial de hiperemia conjuntival, queilite, edema das mãos e dos pés e exantema polimorfo das extremidades. Os exames complementares de diagnóstico demonstraram elevação da proteína C reativa, hiponatremia, hipoalbuminemia, piúria estéril e meningite assética. Perante suspeita de doença de Kawasaki, e apesar de um ecocardiograma inicial normal, foi iniciada imunoglobulina endovenosa ao quinto dia. O ecocardiograma foi repetido ao sétimo dia, revelando sinais de pancardite e ectasia das artérias coronárias, tendo sido iniciado ácido acetilsalicílico. O rapaz teve alta, mas foi reinternado oito dias depois por agravamento da ectasia das coronárias para tratamento com corticoide, que manteve durante quatro semanas. Apresentou normalização das alterações cardíacas aos cinco meses de seguimento, sem novas intercorrências.  Comentários:  A doença de Kawasaki em idade inferior a seis meses é rara e caracteriza-se por evolução mais grave e maior risco de desenvolvimento de aneurisma das artérias coronárias. É importante reconhecer os critérios clínicos e laboratoriais associados a esta entidade, de forma a implementar um tratamento precoce e evitar complicações cardíacas.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[coronary artery ectasia]]></kwd>
<kwd lng="en"><![CDATA[infant]]></kwd>
<kwd lng="en"><![CDATA[Kawasaki disease]]></kwd>
<kwd lng="pt"><![CDATA[doença de Kawasaki]]></kwd>
<kwd lng="pt"><![CDATA[ectasia das artérias coronárias]]></kwd>
<kwd lng="pt"><![CDATA[lactente]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Dionne]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Burns]]></surname>
<given-names><![CDATA[JC]]></given-names>
</name>
<name>
<surname><![CDATA[Dahdah]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Tremoulet]]></surname>
<given-names><![CDATA[AH]]></given-names>
</name>
<name>
<surname><![CDATA[Gauvreau]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[de Ferranti]]></surname>
<given-names><![CDATA[SD]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Treatment Intensification in Patients with Kawasaki Disease and Coronary Aneurysm at Diagnosis]]></article-title>
<source><![CDATA[Pediatrics]]></source>
<year>2019</year>
<volume>143</volume>
</nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Toole]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Frank]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Atypical or Incomplete Kawasaki Disease in a Young Child A Case Report]]></article-title>
<source><![CDATA[J Pediatr Health Care]]></source>
<year>2019</year>
<volume>33</volume>
<page-range>485-8</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Morrison]]></surname>
<given-names><![CDATA[JM]]></given-names>
</name>
<name>
<surname><![CDATA[Inkisar]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Grageda]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Graziano]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Belnekar]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Acute Immune Hemolytic Anemia after administration of high dose IVIG in a child with]]></article-title>
<source><![CDATA[Kawasaki disease]]></source>
<year>2018</year>
<volume>142</volume>
<page-range>474</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Dallaire]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
<name>
<surname><![CDATA[Fortier-Morissette]]></surname>
<given-names><![CDATA[Z]]></given-names>
</name>
<name>
<surname><![CDATA[Blais]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Dhanrajani]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Basodan]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Renaud]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Aspirin Dose and Prevention of Coronary Abnormalities in Kawasaki Disease]]></article-title>
<source><![CDATA[Pediatrics]]></source>
<year>2017</year>
<volume>139</volume>
</nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Petrarca]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Nenna]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Versacci]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Frassanito]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Cangiano]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Nicolai]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Difficult diagnosis of atypical Kawasaki disease in an infant younger than six months a case report]]></article-title>
<source><![CDATA[Italian Journal of Pediatrics]]></source>
<year>2017</year>
<volume>43</volume>
<page-range>30</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Yu]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Diagnosis of incomplete Kawasaki disease]]></article-title>
<source><![CDATA[Korean J Pediatr]]></source>
<year>2012</year>
<volume>55</volume>
<page-range>83-7</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Pinches]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Dobbins]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Cantrell]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[May]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Lopreiato]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Asymptomatic Kawasaki Disease in a 3-Month-Old Infant]]></article-title>
<source><![CDATA[Pediatrics]]></source>
<year>2016</year>
<volume>138</volume>
</nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Shulman]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Rowley]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<source><![CDATA[Kawasaki Disease. Unclassified Infectious Diseases]]></source>
<year>2017</year>
<volume>77</volume>
<page-range>759-72</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Thors]]></surname>
<given-names><![CDATA[VS]]></given-names>
</name>
<name>
<surname><![CDATA[Vastert]]></surname>
<given-names><![CDATA[SJ]]></given-names>
</name>
<name>
<surname><![CDATA[Wulffraat]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[van Royen]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Frenkel]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Periodic fever in MVK Deficiency A Patient Initially Diagnosed with Incomplete Kawasaki Disease]]></article-title>
<collab>de Sain-van der Velden M</collab>
<source><![CDATA[Pediatrics]]></source>
<year>2014</year>
<volume>133</volume>
<page-range>e461-5</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<collab>Burgner DP and Newburger JW</collab>
<article-title xml:lang=""><![CDATA[Etanercept as Adjunctive Primary Therapy in Kawasaki Disease]]></article-title>
<source><![CDATA[Pediatrics]]></source>
<year>2019</year>
<volume>143</volume>
</nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Sundel]]></surname>
<given-names><![CDATA[R.]]></given-names>
</name>
</person-group>
<source><![CDATA[Incomplete (atypical) Kawasaki Disease.]]></source>
<year>2018</year>
</nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Elsevier]]></surname>
<given-names><![CDATA[BV.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Clinical Overview on Kawasaki disease]]></article-title>
<source><![CDATA[Elsevier]]></source>
<year>2018</year>
</nlm-citation>
</ref>
<ref id="B13">
<label>13</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Jordan-Villegas]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Chang]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Ramillo]]></surname>
<given-names><![CDATA[O]]></given-names>
</name>
<name>
<surname><![CDATA[Mejias]]></surname>
<given-names><![CDATA[A.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Concomitant Respiratory Viral Infections in Children with Kawasaki Disease]]></article-title>
<source><![CDATA[Pediatr Infect Dis J.]]></source>
<year>2010</year>
<volume>29</volume>
<page-range>770-2</page-range></nlm-citation>
</ref>
<ref id="B14">
<label>14</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Sundel]]></surname>
<given-names><![CDATA[R.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Kawasaki Disease: clinical features and diagnosis]]></article-title>
<source><![CDATA[UpToDate]]></source>
<year>2018</year>
</nlm-citation>
</ref>
</ref-list>
</back>
</article>
