<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0872-0754</journal-id>
<journal-title><![CDATA[Nascer e Crescer]]></journal-title>
<abbrev-journal-title><![CDATA[Nascer e Crescer]]></abbrev-journal-title>
<issn>0872-0754</issn>
<publisher>
<publisher-name><![CDATA[Centro Hospitalar do Porto]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0872-07542022000400377</article-id>
<article-id pub-id-type="doi">10.25753/birthgrowthmj.v31.i4.22180</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Incomplete Kawasaki disease presenting as complicated acute tonsillitis]]></article-title>
<article-title xml:lang="pt"><![CDATA[Doença de Kawasaki incompleta: Apresentação como amigdalite aguda complicada]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Pissarra]]></surname>
<given-names><![CDATA[Rita]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Amorim]]></surname>
<given-names><![CDATA[Rita]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Catarino]]></surname>
<given-names><![CDATA[Sara]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Marques]]></surname>
<given-names><![CDATA[Joana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodrigues]]></surname>
<given-names><![CDATA[Mariana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Tavares]]></surname>
<given-names><![CDATA[Margarida]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Brito]]></surname>
<given-names><![CDATA[Iva]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Centro Hospitalar Universitário de São João Department of Pediatrics ]]></institution>
<addr-line><![CDATA[Porto ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Centro Hospitalar Universitário de São João Department of Otorhinolaryngology ]]></institution>
<addr-line><![CDATA[Porto ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Universidade do Porto Faculty of Medicine Department of Surgery and Physiology, Otorhinolaryngology]]></institution>
<addr-line><![CDATA[Porto ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Centro Hospitalar Universitário São João Pediatric Rheumatology Unit ]]></institution>
<addr-line><![CDATA[Porto ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af5">
<institution><![CDATA[,Centro Hospitalar Universitário de São João Infectious diseases and Immunodeficiencies Pediatric Unit ]]></institution>
<addr-line><![CDATA[Porto ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>30</day>
<month>12</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>30</day>
<month>12</month>
<year>2022</year>
</pub-date>
<volume>31</volume>
<numero>4</numero>
<fpage>377</fpage>
<lpage>381</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S0872-07542022000400377&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S0872-07542022000400377&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S0872-07542022000400377&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Introduction:  Kawasaki disease (KD) is one of the most common vasculitides in childhood and may cause serious complications, namely coronary artery aneurism (CAA). KD may initially present with fever and otorhinolaryngological manifestations only, which may be misdiagnosed as deep neck infections.  Case report:  A four-year-old female was admitted for complicated acute tonsillitis. Cervical computed tomography suggested an early retropharyngeal abscess. She received intravenous antibiotics and underwent two surgical procedures, without improvement. On day ten of fever, non-specific generalized rash and hand edema were noted, raising suspicion of incomplete KD. Echocardiogram revealed CAA. The girl was treated with intravenous immunoglobulin and corticosteroids, with clinical and laboratory improvement and CAA rapid and persistent resolution.  Discussion:  Suspected complicated tonsillitis failing to respond to adequate treatment should raise suspicion of KD. Prompt treatment is critical to reducing cardiovascular sequelae. Two to three clinical criteria with supplemental laboratory criteria or a positive echocardiogram confirm the diagnosis of incomplete KD.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo  Introdução:  A doença de Kawasaki (DK) é uma das vasculites pediátricas mais comuns, podendo ter complicações importantes, nomeadamente aneurisma coronário (AC). Pode apresentar-se apenas com febre e manifestações otorrinológicas, que podem ser erradamente interpretadas como infeções cervicais profundas.  Caso clínico:  Uma criança do sexo feminino de quatro anos de idade foi internada por suspeita de amigdalite aguda complicada. A tomografia computorizada cervical sugeriu abcesso retrofaríngeo inicial. A criança foi tratada com antibióticos endovenosos e submetida a duas intervenções cirúrgicas, sem melhoria. Ao 10º dia de febre, o aparecimento de exantema generalizado e edema das mãos levantou suspeita de DK incompleta. O ecocardiograma revelou AC. A criança foi tratada com imunoglobulina endovenosa e corticoterapia, com melhoria clínica e laboratorial e regressão rápida e persistente do AC.  Discussão:  O índice de suspeição de DK deve manter-se elevado perante casos de suspeita de amigdalite complicada sem resposta a tratamento adequado. O tratamento precoce é essencial para reduzir sequelas cardiovasculares. Dois ou três critérios com análises/ecocardiograma compatíveis confirmam o diagnóstico de DK incompleta.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[mucocutaneous lymph node syndrome]]></kwd>
<kwd lng="en"><![CDATA[retropharyngeal abscess]]></kwd>
<kwd lng="en"><![CDATA[tonsillitis]]></kwd>
<kwd lng="pt"><![CDATA[abcesso retrofaríngeo]]></kwd>
<kwd lng="pt"><![CDATA[amigdalite aguda]]></kwd>
<kwd lng="pt"><![CDATA[doença de Kawasaki]]></kwd>
<kwd lng="pt"><![CDATA[infeção cervical profunda]]></kwd>
</kwd-group>
</article-meta>
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