<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0872-8178</journal-id>
<journal-title><![CDATA[Jornal Português de Gastrenterologia ]]></journal-title>
<abbrev-journal-title><![CDATA[J Port Gastrenterol.]]></abbrev-journal-title>
<issn>0872-8178</issn>
<publisher>
<publisher-name><![CDATA[Sociedade Portuguesa de Gastrenterologia]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0872-81782007000400004</article-id>
<title-group>
<article-title xml:lang="pt"><![CDATA[Diarreia num doente com imunodeficiência comum variável: a propósito de um caso clínico]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Torres]]></surname>
<given-names><![CDATA[J.]]></given-names>
</name>
<xref ref-type="aff" rid="A01"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Fortuna]]></surname>
<given-names><![CDATA[J.]]></given-names>
</name>
<xref ref-type="aff" rid="A02"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Trigo]]></surname>
<given-names><![CDATA[E.]]></given-names>
</name>
<xref ref-type="aff" rid="A02"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Lopes]]></surname>
<given-names><![CDATA[A.M.]]></given-names>
</name>
<xref ref-type="aff" rid="A03"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Campos]]></surname>
<given-names><![CDATA[M.J.]]></given-names>
</name>
<xref ref-type="aff" rid="A01"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ferreira]]></surname>
<given-names><![CDATA[M.R.]]></given-names>
</name>
<xref ref-type="aff" rid="A02"/>
</contrib>
</contrib-group>
<aff id="A01">
<institution><![CDATA[,Centro Hospitalar de Coimbra Serviço de Gastrenterologia ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
</aff>
<aff id="A02">
<institution><![CDATA[,Centro Hospitalar de Coimbra Serviço de Medicina Interna ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
</aff>
<aff id="A03">
<institution><![CDATA[,Centro de Saúde Norton de Matos Serviço de Medicina Geral e Familiar ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>09</month>
<year>2007</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>09</month>
<year>2007</year>
</pub-date>
<volume>14</volume>
<numero>4</numero>
<fpage>199</fpage>
<lpage>203</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S0872-81782007000400004&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S0872-81782007000400004&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S0872-81782007000400004&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="pt"><p><![CDATA[A imunodeficiência comum variável corresponde a um grupo heterogéneo de doenças imunológicas de etiologia desconhecida, caracterizada por uma resposta da imunidade humoral e celular prejudicadas, o que clinicamente se traduz por um aumento na incidência de infecções recorrentes, fenómenos auto-imunes e doenças neoplásicas. Os autores apresentam o caso clínico de uma doente com diagnóstico de imunodeficiência comum variável, internada para estudo de diarreia e emagrecimento.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Common variable immunodeficiency represents a heterogeneous group of immunologic disorders of unknown aetiology, characterized by impaired antibody and cell-mediated responses and clinically manifested by recurrent infections, autoimmune disease and malignancy. The authors present a clinical case of a patient with common variable immunodeficiency admitted for diarrhea and weight loss.]]></p></abstract>
</article-meta>
</front><body><![CDATA[ <p><b>Diarreia num doente com imunodefici&ecirc;ncia comum vari&aacute;vel:      a prop&oacute;sito de um caso cl&iacute;nico</b></p>        <p>&nbsp;</p>        <p>J. Torres<sup><a href="#1">1</a><a name="top1"></a></sup>, J. Fortuna<sup><a href="#2">2</a></sup>,    E. Trigo<sup><a href="#2">2</a><a name="top2"></a></sup>, A.M. Lopes<sup><a href="#3">3</a></sup>,    M.J. Campos<sup><a href="#1">1</a></sup>, M.R. Ferreira<sup><a href="#2">2</a><a name="top3"></a></sup></p>      <p>&nbsp;</p>      <p><b>Resumo</b></p>      <p>A imunodeficiência comum variável corresponde a um grupo heterogéneo de doenças imunológicas de etiologia desconhecida, caracterizada por uma resposta da imunidade humoral e celular prejudicadas, o que clinicamente se traduz por um aumento na incidência de infecções recorrentes, fenómenos auto-imunes e doenças neoplásicas. Os autores apresentam o caso clínico de uma doente com diagnóstico de imunodeficiência comum variável, internada para estudo de diarreia e emagrecimento.</p>      <p>&nbsp;</p>     <p><b>Summary</b></p>      <p>Common variable immunodeficiency represents a heterogeneous group of immunologic    disorders of unknown aetiology, characterized by impaired antibody and cell-mediated    responses and clinically manifested by recurrent infections, autoimmune disease    and malignancy. The authors present a clinical case of a patient with common    variable immunodeficiency admitted for diarrhea and weight loss.</p>      <p>&nbsp;</p>      ]]></body>
<body><![CDATA[<p>&nbsp;</p>      <p>Texto Completo disponível apenas em PDF</p>      <p>Full text only available in PDF format</p>      <p>&nbsp;</p>      <p>&nbsp;</p>      <p>BIBLIOGRAFIA</p>      <!-- ref --><p>1. Kainulainen L, Nikoskelainen J, Ruuskanen O. Diagnostic findings in 95 Finnish patients with Common Variable Immunodeficiency. J Clin Immunol 2001; 21: 145-149.&nbsp;&nbsp;&nbsp;&nbsp;&nbsp;&nbsp;&nbsp;&nbsp;[&#160;<a href="javascript:void(0);" onclick="javascript: window.open('/scielo.php?script=sci_nlinks&ref=000019&pid=S0872-8178200700040000400001&lng=','','width=640,height=500,resizable=yes,scrollbars=1,menubar=yes,');">Links</a>&#160;]<!-- end-ref --><p>2. Sneller MC, Strober W, Einsensten E, Jaffe JS, Cunningham-Ruddles C. New insights into common variable immunodeficiency. Ann Inter Medicine 1993; 118 (9): 720-730.</p>      <p>3. Weiler C, Bankers-Fulbright J. Common Variable Immunodeficiency: Test indications and interpretations. Mayo Clin Proc. 2005; 80 (9): 1187-1200.</p>      <p>4. Bonilla F, Geha RF. Update on Primary Immunodeficiency diseases. J Allergy Clin Immunol. 2006; 117: 435- 441.</p>      ]]></body>
<body><![CDATA[<p>5. Kokron C, Errante P, Barros TM, Baracho G, Camargo M, Kalil J, <i>et al</i>.    Clinical and laboratory aspects of Common Variable Immunodeficiency. Ann Brazilian    Acad Sciences. 2004; 76 (4): 707- 726.</p>      <p>6. Zenote T, Souillet G. Cancer and primary humoral immunodeficiency. Bull Cancer. 1997. 84: 813-821.</p>      <p>7. Kinlen LJ, Webster AD, Bird AG, <i>et al</i>. Prospective study of cancer in patients with hipogammaglobulinaemia. Lancet 1985; 1: 263-266.</p>      <p>8. Rosen FS, Cooper MD, Wedgwood RJP. The Primary Immunodeficiencies. N Eng J Med. 1995; 333 (7): 431- 440.</p>      <p>9. Kalha I, Sellin JH. Common Variable Immunodeficiency and the Gastrointestinal Tract. Current Gastroenterology Reports 2004; 6:377-383.</p>      <p>10. Onbasi Kevser, Gunsar Fulya, <i>et al</i>. Common variable Immunodeficiency presenting with malabsortion due to giardiasis. Turk J Gastrenterol 2005; 16 (2): 111-113.</p>      <p>11. Lai Ping So A, Mayer L. Gastrointestinal manifestations of Primary Immunodeficiency disorders. Semin Gastroint Dis. 1997; 8: 22-32.</p>      <p><i>&nbsp;</i></p>     <p>&nbsp;</p>     <p><sup><a name="1"></a>(<a href="#top1">1</a>)</sup> Serviço de Gastrenterologia.</p>     ]]></body>
<body><![CDATA[<p><sup><a name="2"></a>(<a href="#top2">2</a>)</sup> Serviço de Medicina Interna.    Centro Hospitalar de Coimbra, Coimbra, Portugal.</p>     <p><sup><a name="3"></a>(<a href="#top3">3</a>)</sup> Serviço de Medicina Geral    e Familiar, Centro de Saúde Norton de Matos, Coimbra, Portugal.</p>      <p>&nbsp;</p>     <p><i>Correspondência:</i></p>     <p>Joana Torres</p>     <p>Centro Hospitalar de Coimbra</p>     <p>Serviço de Gastrenterologia</p>     <p>Quinta dos Vales, São Martinho do Bispo</p>     <p>3046-853 Coimbra</p>     <p>Tel.: 919740545</p>     ]]></body>
<body><![CDATA[<p><i>e-mail</i>: <a href="mailto:joanatorres00@hotmail.com">joanatorres00@hotmail.com</a></p>     <p>&nbsp;</p>      <p align="right"><i>Recebido para publicação: 10/10/2006</i></p>     <p align="right"><i>Aceite para publicação: 20/06/2007</i></p>       ]]></body><back>
<ref-list>
<ref id="B1">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Kainulainen]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Nikoskelainen]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Ruuskanen]]></surname>
<given-names><![CDATA[O]]></given-names>
</name>
</person-group>
<article-title xml:lang="en"><![CDATA[Diagnostic findings in 95 Finnish patients with Common Variable Immunodeficiency]]></article-title>
<source><![CDATA[J Clin Immunol]]></source>
<year>2001</year>
<volume>21</volume>
<page-range>145-149</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
