Mediastinal cystic lymphangioma

Sandra Saleiro ¹

Adriana Magalhães ²

Conceição Souto Moura ³

Venceslau Hespanhol ⁴

Resumo

O linfangioma mediastínico é uma neoplasia vascular rara, correspondendo a 0,7 a 4,5% de todos os tumores do mediastino. É um tumor benigno, que ocorre geralmente como uma massa mediastínica de crescimento lento. A maioria dos doentes está assintomática, sendo diagnosticado incidentalmente, após a realização de uma radiografia torácica de rotina. O tratamento de eleição consiste na ressecção cirúrgica completa. O prognóstico depende do grau de ressecabilidade e, se a lesão for totalmente removida, não se esperam recidivas.

Abstract

Mediastinal lymphangioma is a rare vascular neoplasm, accounting for 0.7 to 4.5% of all the mediastinum tumors. It is a benign tumor, generally occurring as a mediastinal mass of slow growth. Most patients are asymptomatic, being incidentally diagnosed after a routine chest radiograph. The best treatment consists of complete surgical resection. Prognosis depends on the degree of resecability degree, and recurrence is not expected if the lesion is totally removed.

Key-words: Mediastinal tumor, lymphangioma, mediastinal cyst.

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² Assistente Hospitalar Graduada de Pneumologia

³ Assistente Hospitalar de Anatomia Patológica

⁴ Chefe de Serviço de Pneumologia e Professor Auxiliar com Agregação da Faculdade de Medicina da Universidade do Porto

Hospital de São João, Porto

Serviço de Pneumologia. Director de Serviço: Professor Doutor José Agostinho Marques

Serviço de Anatomia Patológica. Directora de Serviço: Professora Doutora Fátima Carneiro

Hospital de São João

4200-451 Porto

Telefone: 225512215

e-mail: sandrasaleiro@portugalmail.pt

Recebido para publicação/received for publication: 06.06.06

Aceite para publicação/accepted for publication: 06.07.21