<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1646-2890</journal-id>
<journal-title><![CDATA[Revista Portuguesa de Estomatologia, Medicina Dentária e Cirurgia Maxilofacial]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Port Estomatol Med Dent Cir Maxilofac]]></abbrev-journal-title>
<issn>1646-2890</issn>
<publisher>
<publisher-name><![CDATA[Sociedade Portuguesa de Estomatologia e Medicina Dentária]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1646-28902022000200099</article-id>
<article-id pub-id-type="doi">10.24873/j.rpemd.2022.06.867</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Malignant peripheral nerve sheath tumor with rhabdoid features arising in the temporal region of a patient suffering from neurofibromatosis 1 - A case report]]></article-title>
<article-title xml:lang="pt"><![CDATA[Tumor maligno da bainha do nervo periférico com características rabdoides surgindo na região temporal de um paciente com neurofibromatose 1 - Caso clínico]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Amer]]></surname>
<given-names><![CDATA[Hatem Wael]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Shaheen]]></surname>
<given-names><![CDATA[Hamed Abdelwahab]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ashoub]]></surname>
<given-names><![CDATA[Madiha Nabil]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Mahmoud]]></surname>
<given-names><![CDATA[Sarah Ahmed Mohamed]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Cairo University Faculty of Dentistry Oral &amp; Maxillofacial Pathology Department]]></institution>
<addr-line><![CDATA[Cairo ]]></addr-line>
<country>Egypt</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Naser Health Institute Craniomaxillofacial Program ]]></institution>
<addr-line><![CDATA[Cairo ]]></addr-line>
<country>Egypt</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Misr International University Faculty of Oral and Dental Medicine Oral Pathology Department]]></institution>
<addr-line><![CDATA[Cairo ]]></addr-line>
<country>Egypt</country>
</aff>
<pub-date pub-type="pub">
<day>30</day>
<month>06</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>30</day>
<month>06</month>
<year>2022</year>
</pub-date>
<volume>63</volume>
<numero>2</numero>
<fpage>99</fpage>
<lpage>104</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S1646-28902022000200099&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S1646-28902022000200099&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S1646-28902022000200099&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract The malignant peripheral nerve sheath tumor is one of the rare sarcomas that have a challenging diagnosis. It occurs independently with neurofibromatosis type 1. Some studies referred that malignant peripheral nerve sheath tumor attains a worse prognosis when it occurs in the head and neck region. In the reported case, a male patient with neurofibromatosis type 1 manifestations presented with a large mass in the temporal region. Based on the clinical history, histopathology, and immunohistochemical findings, the lesion was diagnosed as a low-grade malignant peripheral nerve sheath tumor with rhabdoid features. Surgical resection followed by intensity-modulated radiotherapy was the treatment of choice.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo O tumor maligno da bainha do nervo periférico é um dos raros sarcomas que têm um diagnóstico desafiador. Ocorre independentemente com a neurofibromatose tipo 1. Alguns estudos referem que o tumor maligno da bainha do nervo periférico apresenta pior prognóstico quando ocorre na região da cabeça e pescoço. No caso relatado, um paciente do sexo masculino com manifestações de neurofibromatose tipo 1 apresentou uma grande massa na região temporal. Com base na história, histopatologia e achados imuno-histoquímicos, a lesão foi diagnosticada como um tumor maligno de bainha de nervo periférico de baixo grau com características rabdoides. A ressecção cirúrgica seguida de radioterapia de intensidade modulada foi o tratamento de escolha.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Head]]></kwd>
<kwd lng="en"><![CDATA[Malignant peripheral nerve sheath tumor]]></kwd>
<kwd lng="en"><![CDATA[Malignant triton tumor]]></kwd>
<kwd lng="en"><![CDATA[Neurofibromatosis 1]]></kwd>
<kwd lng="pt"><![CDATA[Cabeça]]></kwd>
<kwd lng="pt"><![CDATA[Tumor maligno da bainha do nervo]]></kwd>
<kwd lng="pt"><![CDATA[Periférico]]></kwd>
<kwd lng="pt"><![CDATA[Tumor de Tritão maligno]]></kwd>
<kwd lng="pt"><![CDATA[Neurofibromatose 1]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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