<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1646-2890</journal-id>
<journal-title><![CDATA[Revista Portuguesa de Estomatologia, Medicina Dentária e Cirurgia Maxilofacial]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Port Estomatol Med Dent Cir Maxilofac]]></abbrev-journal-title>
<issn>1646-2890</issn>
<publisher>
<publisher-name><![CDATA[Sociedade Portuguesa de Estomatologia e Medicina Dentária]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1646-28902024000200066</article-id>
<article-id pub-id-type="doi">10.24873/j.rpemd.2024.06.1221</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Oral health status and oral habits: A study on 33 rare diseases]]></article-title>
<article-title xml:lang="pt"><![CDATA[Estado e hábitos de saúde oral: Um estudo em 33 doenças raras]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Nunes]]></surname>
<given-names><![CDATA[Diana Oliveira]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Pinto]]></surname>
<given-names><![CDATA[Ana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Albuquerque]]></surname>
<given-names><![CDATA[Teresa]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Luís]]></surname>
<given-names><![CDATA[Henrique]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Graça]]></surname>
<given-names><![CDATA[Sandra Ribeiro]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Bizarra]]></surname>
<given-names><![CDATA[Fátima]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidade de Lisboa Faculdade de Medicina Dentária ]]></institution>
<addr-line><![CDATA[Lisbon ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>06</month>
<year>2024</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>06</month>
<year>2024</year>
</pub-date>
<volume>65</volume>
<numero>2</numero>
<fpage>66</fpage>
<lpage>75</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S1646-28902024000200066&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S1646-28902024000200066&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S1646-28902024000200066&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Objectives:  To analyze the patient profile and characterize the oral health status, oral habits, and daily oral hygiene difficulties of individuals with rare diseases.  Methods:  Data were collected from records of the clinic for people with disabilities at the Faculdade de Medicina Dentária da Universidade de Lisboa, using the Decayed, Missing, and Filled Teeth index, the simplified debris index, and the bleeding index.  Results:  The sample comprised 64 individuals with 33 different rare diseases, with a mean age of 31.5(±10.29) years, predominantly male (54.7%). Most could move without difficulty (51.6%), required assistance in activities of daily living (60.9%), and were cooperative in oral hygiene (54.7%). Also, 40.6% could not communicate. Half of the sample brushed their teeth twice a day, with 18.8% being independent in this activity, and the most common toothbrushing difficulty was not being able to rinse (53.1%). The Decayed, Missing, and Filled Teeth index was 8.81 (±7.54), with a higher number of filled teeth (4.47; ±5.35). The bleeding índex had a mean of 1.23 (±0.56), and the simplified debris index had a mean value of 1.62 (±0.78).  Conclusions:  The population studied expresses care for oral health and treatment.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Re s u m o  Objetivos:  Analisar o perfil dos pacientes e caracterizar o estado de saúde oral, os hábitos orais e as dificuldades na higiene oral diária de indivíduos com doenças raras.  Métodos:  Os dados foram recolhidos dos registos da Clínica para Pessoas com Deficiência da Faculdade de Medicina Dentária da Universidade de Lisboa, utilizando o índice de dentes permanentes cariados, perdidos e obturados, o índice de higiene oral simplificado e o índice de hemorragia.  Resultados:  A amostra foi constituída por 64 indivíduos com 33 doenças raras diferentes, com uma média de idades de 31,5 (±10,29) anos, predominantemente do género masculino (54,7%). A maioria era capaz de se deslocar sem dificuldade (51,6%), era dependente nas atividades de vida diária (60,9%) e era cooperante nas consultas de higiene oral (54,7%). Além disso, 40,6% eram incapazes de comunicar. A escovagem dos dentes duas vezes por dia era feita por metade da amostra, sendo que 18,8% eram independentes nesta atividade, e a dificuldade mais comum era não conseguir bochechar (53,1%). O índice de dentes cariados, perdidos e obturados foi de 8,81 (±7,54), com maior número de dentes obturados (4,47; ±5,35). O índice de hemorragia teve um valor médio de 1,23 (±0,56) e o índice de higiene oral simplificado teve um valor médio de 1,62 (±0,78).  Conclusões:  A população estudada manifesta preocupação com a saúde e o tratamento oral.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Oral health]]></kwd>
<kwd lng="en"><![CDATA[Oral hygiene]]></kwd>
<kwd lng="en"><![CDATA[Rare disease]]></kwd>
<kwd lng="en"><![CDATA[Syndrome]]></kwd>
<kwd lng="en"><![CDATA[Toothbrushing]]></kwd>
<kwd lng="pt"><![CDATA[Saúde oral]]></kwd>
<kwd lng="pt"><![CDATA[Higiene oral]]></kwd>
<kwd lng="pt"><![CDATA[Doença rara]]></kwd>
<kwd lng="pt"><![CDATA[Síndrome]]></kwd>
<kwd lng="pt"><![CDATA[Escovagem dentária]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Baldovino]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Moliner]]></surname>
<given-names><![CDATA[AM]]></given-names>
</name>
<name>
<surname><![CDATA[Taruscio]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Daina]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Roccatello]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Rare Diseases in Europe: from a Wide to a Local Perspective]]></article-title>
<source><![CDATA[Isr Med Assoc J]]></source>
<year>2016</year>
<volume>18</volume>
<page-range>359-63</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Moliner]]></surname>
<given-names><![CDATA[AM]]></given-names>
</name>
<name>
<surname><![CDATA[Waligora]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[The European Union policy in the field of rare diseases]]></article-title>
<source><![CDATA[Adv Exp Med Biol]]></source>
<year>2017</year>
<volume>1031</volume>
<page-range>561-87</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[About Rare Diseases]]></article-title>
<source><![CDATA[Orphanet]]></source>
<year>2024</year>
</nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Molina-García]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Castellanos-Cosano]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Machuca-Portillo]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Paz]]></surname>
<given-names><![CDATA[MP]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Impact of rare diseases in oral health]]></article-title>
<source><![CDATA[Med Oral Patol Oral Cir Bucal]]></source>
<year>2016</year>
<volume>21</volume>
<page-range>e587-94</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Souza]]></surname>
<given-names><![CDATA[ÍP]]></given-names>
</name>
<name>
<surname><![CDATA[Androlage]]></surname>
<given-names><![CDATA[JS]]></given-names>
</name>
<name>
<surname><![CDATA[Bellato]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Barsaglini]]></surname>
<given-names><![CDATA[RA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[A qualitative approach to rare genetic diseases: an integrative review of the national and international literature]]></article-title>
<source><![CDATA[Cien Saude Colet]]></source>
<year>2019</year>
<volume>24</volume>
<page-range>3683-700</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Nguengang]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Lambert]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Olry]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Estimating cumulative point prevalence of rare diseases: analysis of the Orphanet database]]></article-title>
<source><![CDATA[Eur J Hum Genet]]></source>
<year>2020</year>
<volume>28</volume>
<page-range>165-73</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<collab>National Institutes of Health</collab>
<article-title xml:lang=""><![CDATA[Oral Health in America: Advances and challenges]]></article-title>
<source><![CDATA[National Institutes of Health, National Institute of Dental and Craniofacial Research]]></source>
<year>2021</year>
</nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Baliga]]></surname>
<given-names><![CDATA[MS]]></given-names>
</name>
<name>
<surname><![CDATA[Deshpande]]></surname>
<given-names><![CDATA[MA]]></given-names>
</name>
<name>
<surname><![CDATA[Thosar]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Rathi]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Bane]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Deulkar]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Comparison of impact of oral hygiene instructions given via sign language and validated customized Oral Health Education Skit Video on Oral Hygiene Status of children with hearing impairment]]></article-title>
<source><![CDATA[J Indian Soc Pedod Prev Dent]]></source>
<year>2020</year>
<volume>38</volume>
<page-range>20-5</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bizarra]]></surname>
<given-names><![CDATA[MF]]></given-names>
</name>
<name>
<surname><![CDATA[Graça]]></surname>
<given-names><![CDATA[SR]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[O perfil do Paciente da consulta para Pessoas com Necessidades Especiais da FMDUL]]></article-title>
<source><![CDATA[Rev Port Estomatol Med Dent Cir Maxilofac]]></source>
<year>2010</year>
<volume>51</volume>
<page-range>69-74</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Singh]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Agarwal]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Aeran]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Dhawan]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Oral Health and Quality of life in Preadolescents with hearing impairment in Uttarakhand, India]]></article-title>
<source><![CDATA[J Oral Biol Craniofac Res]]></source>
<year>2019</year>
<volume>9</volume>
<page-range>161-5</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Esteves]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Mendes]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Bernardo]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Oral health status of na institutionalized population with profound disability]]></article-title>
<source><![CDATA[Rev Port Estomatol Med Dent Cir Maxilofac]]></source>
<year>2021</year>
<volume>58</volume>
<page-range>146-52</page-range></nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Aureliano]]></surname>
<given-names><![CDATA[WA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Trajetórias Terapêuticas Familiares: Doenças Raras Hereditárias Como Sofrimento de Longa Duração]]></article-title>
<source><![CDATA[Cien Saude Colet]]></source>
<year>2018</year>
</nlm-citation>
</ref>
<ref id="B13">
<label>13</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Hanisch]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Hoffmann]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Bohner]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Hanisch]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Benz]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Kleinheinz]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Rare diseases with periodontal manifestations]]></article-title>
<source><![CDATA[Int J Environ Res Public Health]]></source>
<year>2019</year>
<volume>16</volume>
<page-range>867</page-range></nlm-citation>
</ref>
<ref id="B14">
<label>14</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Jin]]></surname>
<given-names><![CDATA[EYW]]></given-names>
</name>
<name>
<surname><![CDATA[Daly]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[The self-reported oral health status and behaviors of adults who are deaf and blind]]></article-title>
<source><![CDATA[Spec Care Dentist]]></source>
<year>2010</year>
<volume>30</volume>
<page-range>8-13</page-range></nlm-citation>
</ref>
<ref id="B15">
<label>15</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Friedlander]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Vincent]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Berdal]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Cormier-Daire]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
<name>
<surname><![CDATA[Lyonnet]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Garcelon]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Consideration of oral health in rare disease expertise centres: a retrospective study on 39 rare diseases using text mining extraction method]]></article-title>
<source><![CDATA[Orphanet J Rare Dis]]></source>
<year>2022</year>
<volume>17</volume>
<page-range>317</page-range></nlm-citation>
</ref>
<ref id="B16">
<label>16</label><nlm-citation citation-type="book">
<collab>World Health Organization</collab>
<source><![CDATA[Oral Health Surveys. Basic Methods]]></source>
<year>2013</year>
<edition>5</edition>
<publisher-loc><![CDATA[Geneva ]]></publisher-loc>
<publisher-name><![CDATA[World Health Organization]]></publisher-name>
</nlm-citation>
</ref>
<ref id="B17">
<label>17</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Löe]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Silness]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Periodontal disease in pregnancy: prevalence and severity]]></article-title>
<source><![CDATA[Acta Odontol Scand]]></source>
<year>1963</year>
<volume>21</volume>
<page-range>533-51</page-range></nlm-citation>
</ref>
<ref id="B18">
<label>18</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Greene]]></surname>
<given-names><![CDATA[JC]]></given-names>
</name>
<name>
<surname><![CDATA[Vermillion]]></surname>
<given-names><![CDATA[JR]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[The simplified oral hygiene index]]></article-title>
<source><![CDATA[J Am Dent Assoc]]></source>
<year>1964</year>
<volume>68</volume>
<page-range>7-13</page-range></nlm-citation>
</ref>
<ref id="B19">
<label>19</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Montez]]></surname>
<given-names><![CDATA[ARH]]></given-names>
</name>
<name>
<surname><![CDATA[Bizarra]]></surname>
<given-names><![CDATA[MF]]></given-names>
</name>
<name>
<surname><![CDATA[Graça]]></surname>
<given-names><![CDATA[SR]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Evaluation of oral characteristics and oral health of individuals with fragile X syndrome and related guardians&#8217; perceptions]]></article-title>
<source><![CDATA[Spec Care Dentist]]></source>
<year>2021</year>
<volume>41</volume>
<page-range>13-9</page-range></nlm-citation>
</ref>
<ref id="B20">
<label>20</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Lai]]></surname>
<given-names><![CDATA[YYL]]></given-names>
</name>
<name>
<surname><![CDATA[Downs]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Zafar]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Wong]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Walsh]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Leonard]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Oral health care and service utilisation in individuals with Rett syndrome: an international cross-sectional study]]></article-title>
<source><![CDATA[J Intellect Disable Res]]></source>
<year>2021</year>
<volume>65</volume>
<page-range>561-76</page-range></nlm-citation>
</ref>
<ref id="B21">
<label>21</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Leroy]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Declerck]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Oral health care utilization in children with disabilities]]></article-title>
<source><![CDATA[Clin Oral Invest]]></source>
<year>2013</year>
<volume>17</volume>
<page-range>1855-61</page-range></nlm-citation>
</ref>
<ref id="B22">
<label>22</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Carneiro]]></surname>
<given-names><![CDATA[NCR]]></given-names>
</name>
<name>
<surname><![CDATA[Monteiro]]></surname>
<given-names><![CDATA[LR]]></given-names>
</name>
<name>
<surname><![CDATA[Pordeus]]></surname>
<given-names><![CDATA[IA]]></given-names>
</name>
<name>
<surname><![CDATA[Borges-Oliveira]]></surname>
<given-names><![CDATA[AC]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Oral sucking habits among children with Down syndrome and cerebral palsy]]></article-title>
<source><![CDATA[Spec Care Dentist]]></source>
<year>2017</year>
<volume>37</volume>
<page-range>176-80</page-range></nlm-citation>
</ref>
<ref id="B23">
<label>23</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Mahdi]]></surname>
<given-names><![CDATA[SS]]></given-names>
</name>
<name>
<surname><![CDATA[Jafri]]></surname>
<given-names><![CDATA[HA]]></given-names>
</name>
<name>
<surname><![CDATA[Allana]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Amenta]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
<name>
<surname><![CDATA[Khawaja]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Qasim]]></surname>
<given-names><![CDATA[SSB]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Oral Manifestations of Rett Syndrome-A Systematic Review]]></article-title>
<source><![CDATA[Int J Environ Res Public Health]]></source>
<year>2021</year>
<volume>18</volume>
<page-range>1162</page-range></nlm-citation>
</ref>
<ref id="B24">
<label>24</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Prado]]></surname>
<given-names><![CDATA[HV]]></given-names>
</name>
<name>
<surname><![CDATA[Carneiro]]></surname>
<given-names><![CDATA[NCR]]></given-names>
</name>
<name>
<surname><![CDATA[Perazzo]]></surname>
<given-names><![CDATA[MF]]></given-names>
</name>
<name>
<surname><![CDATA[Abreu]]></surname>
<given-names><![CDATA[MH]]></given-names>
</name>
<name>
<surname><![CDATA[Martins]]></surname>
<given-names><![CDATA[CC]]></given-names>
</name>
<name>
<surname><![CDATA[Borges-Oliveira]]></surname>
<given-names><![CDATA[AC]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Assessing a possible vulnerability to dental caries in individuals with rare genetic diseases that affect the skeletal development]]></article-title>
<source><![CDATA[Orphanet J Rare Dis]]></source>
<year>2019</year>
<volume>14</volume>
<page-range>145</page-range></nlm-citation>
</ref>
<ref id="B25">
<label>25</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Vettore]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Borges-Oliveira]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Prado]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Lamarca]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Owens]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Rare genetic diseases affecting skeletal development and oral health disparities among children and adolescents: a pathway analysis]]></article-title>
<source><![CDATA[Int Dent J]]></source>
<year>2020</year>
<volume>70</volume>
<page-range>469-76</page-range></nlm-citation>
</ref>
<ref id="B26">
<label>26</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Albahrani]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Alyahya]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Qudeimat]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Toumba]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Salivary fluoride concentration following toothbrushing with and without rinsing: a randomised controlled trial]]></article-title>
<source><![CDATA[BMC Oral Health]]></source>
<year>2022</year>
<volume>22</volume>
<page-range>53</page-range></nlm-citation>
</ref>
<ref id="B27">
<label>27</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Petrovi&#263;]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Koji&#263;]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Mili&#263;]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Luzio]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Peri&#263;]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Markovi&#263;]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Toothpaste ingestion-evaluating the problem and ensuring safety: systematic review and meta-analysis]]></article-title>
<source><![CDATA[Front Public Health]]></source>
<year>2023</year>
<volume>11</volume>
<page-range>1279915</page-range></nlm-citation>
</ref>
<ref id="B28">
<label>28</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Ballesta-Mudarra]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Machuca-Portillo]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Torres-Lagares]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Rodrigues-Caballero]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Yánez-Vico]]></surname>
<given-names><![CDATA[RM]]></given-names>
</name>
<name>
<surname><![CDATA[Solano-Reina]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Determination of periodontopathogens in patients with Cri du chat syndrome]]></article-title>
<source><![CDATA[Med Oral Patol Oral Cir Bucal]]></source>
<year>2013</year>
<volume>18</volume>
</nlm-citation>
</ref>
<ref id="B29">
<label>29</label><nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[III Estudo Nacional de Prevale&#770;ncia das Doenc&#807;as Orais]]></article-title>
<source><![CDATA[Direc&#807;a&#771;o Geral de Sau&#769;de]]></source>
<year>2021</year>
</nlm-citation>
</ref>
<ref id="B30">
<label>30</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Figueira]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Bizarra]]></surname>
<given-names><![CDATA[MF]]></given-names>
</name>
<name>
<surname><![CDATA[Graça]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Evolution of oral status in adults with intellectual and developmental disabilities: a longitudinal study]]></article-title>
<source><![CDATA[Research and Practice in Intellectual and Developmental Disabilities]]></source>
<year>2022</year>
<volume>9</volume>
<page-range>51-60</page-range></nlm-citation>
</ref>
<ref id="B31">
<label>31</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Sjogreen]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Andersson-Norinder]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Bratel]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Oral health and oro-motor function in rare diseases - a database study]]></article-title>
<source><![CDATA[Swed Dent J]]></source>
<year>2015</year>
<volume>39</volume>
<page-range>23-7</page-range></nlm-citation>
</ref>
<ref id="B32">
<label>32</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Pinto]]></surname>
<given-names><![CDATA[AM]]></given-names>
</name>
<name>
<surname><![CDATA[Bizarra]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
<name>
<surname><![CDATA[Graça]]></surname>
<given-names><![CDATA[SR]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Sociodemographic and oral profile of people with disabilities at the clinic of the Faculty of Dental Medicine of the University of Lisbon]]></article-title>
<source><![CDATA[Rev Port Estomatol Med Dent Cir Maxilofac]]></source>
<year>2023</year>
<volume>64</volume>
<page-range>147-54</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
