<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1646-2890</journal-id>
<journal-title><![CDATA[Revista Portuguesa de Estomatologia, Medicina Dentária e Cirurgia Maxilofacial]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Port Estomatol Med Dent Cir Maxilofac]]></abbrev-journal-title>
<issn>1646-2890</issn>
<publisher>
<publisher-name><![CDATA[Sociedade Portuguesa de Estomatologia e Medicina Dentária]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1646-28902024000200094</article-id>
<article-id pub-id-type="doi">10.24873/j.rpemd.2024.06.1216</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[White Sponge Nevus of the oral mucosa - Case report]]></article-title>
<article-title xml:lang="pt"><![CDATA[Nevo Branco Esponjoso da mucosa oral - Relato de caso]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Batalha]]></surname>
<given-names><![CDATA[Beatriz]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Abreu]]></surname>
<given-names><![CDATA[Daniela]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Moreira]]></surname>
<given-names><![CDATA[André]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Freitas]]></surname>
<given-names><![CDATA[Filipe]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Francisco]]></surname>
<given-names><![CDATA[Helena]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Caramês]]></surname>
<given-names><![CDATA[João]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidade de Lisboa Faculdade de Medicina Dentária ]]></institution>
<addr-line><![CDATA[Lisboa ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>06</month>
<year>2024</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>06</month>
<year>2024</year>
</pub-date>
<volume>65</volume>
<numero>2</numero>
<fpage>94</fpage>
<lpage>98</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S1646-28902024000200094&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S1646-28902024000200094&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S1646-28902024000200094&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract White sponge nevus (WSN) is a rare autosomal-dominant disorder of the non-keratinized mucosa, characterized by a thickened white edematous mucosa whose surface appears irregular, wrinkly, or spongy. It affects mainly the oral mucosa. The histopathological examination demonstrates hyperparakeratosis, acanthosis with intracellular edema and vacuolization over the prickle cell layer, and eosinophilic perinuclear condensation. The currently accepted etiology is a mutation of the keratin 4 and/or keratin 13 genes. We present a case of WSN diagnosed in a 30-year-old white male patient with white corrugated bilateral lesions on the buccal mucosa that extended beyond the occlusal plane. A biopsy was obtained, and the histological presentation included superficial parakeratosis, prominent acanthosis of the squamous epithelium, and areas with prominent intracellular edema, which confirmed the diagnosis. No treatment was necessary other than patient counseling and initial 6-month follow-up consultation. His attending dentist was informed of the diagnosis, and further follow-ups were recommended.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo O nevo branco esponjoso (NBE) é uma doença rara, autossómica dominante, da mucosa não queratinizada, que se caracteriza pela presença de uma mucosa espessada e esbranquiçada cuja superfície é irregular, rugosa ou esponjosa. A mucosa oral é a mais afetada. Na avaliação histopatológica apresenta hiper-paraqueratose, acantose com edema e vacuolização intracelulares na camada espinhosa, e condensação eosinofílica perinuclear. Atualmente pensa-se que a etiologia resulta da mutação dos genes da queratina 4 e/ou 13. Apresentamos um caso de um homem, leucodérmico, de 30 anos, com lesões brancas enrugadas bilaterais na mucosa bucal, cuja extensão ultrapassa o plano oclusal. Foi realizada uma biopsia, e a aparência histológica traduziu-se em paraqueratose superficial, com proeminente acantose do epitélio pavimentoso e áreas de proeminente edema intracelular, o que confirmou o diagnóstico. Não foi necessário tratamento, para além do aconselhamento do doente e follow-up inicial de 6 meses. O seu médico dentista foi informado do diagnóstico e recomendou-se manutenção de controlos]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Autosomal dominant disorder]]></kwd>
<kwd lng="en"><![CDATA[Oral mucosa]]></kwd>
<kwd lng="en"><![CDATA[White lesions]]></kwd>
<kwd lng="en"><![CDATA[White sponge nevus]]></kwd>
<kwd lng="pt"><![CDATA[Doença autossómica dominante]]></kwd>
<kwd lng="pt"><![CDATA[Mucosa oral]]></kwd>
<kwd lng="pt"><![CDATA[Lesões brancas]]></kwd>
<kwd lng="pt"><![CDATA[Nevo branco esponjoso]]></kwd>
</kwd-group>
</article-meta>
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