<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1646-5830</journal-id>
<journal-title><![CDATA[Acta Obstétrica e Ginecológica Portuguesa]]></journal-title>
<abbrev-journal-title><![CDATA[Acta Obstet Ginecol Port]]></abbrev-journal-title>
<issn>1646-5830</issn>
<publisher>
<publisher-name><![CDATA[Euromédice, Edições Médicas Lda.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1646-58302022000200166</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Herlyn-Werner-Wunderlich syndrome: a challenging diagnosis]]></article-title>
<article-title xml:lang="pt"><![CDATA[Síndrome de Herlyn-Werner-Wunderlich: um diagnóstico desafiante]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Leite]]></surname>
<given-names><![CDATA[Sara Dias]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Raposo]]></surname>
<given-names><![CDATA[Maria Inês]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Teves]]></surname>
<given-names><![CDATA[Mariana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Lima]]></surname>
<given-names><![CDATA[Ana Furtado]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sampaio]]></surname>
<given-names><![CDATA[Joana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Divino Espírito Santo Department of Gynecology and Obstetrics ]]></institution>
<addr-line><![CDATA[Ponta Delgada ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Divino Espírito Santo Department of Gynecology and Obstetrics ]]></institution>
<addr-line><![CDATA[Ponta Delgada ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital Divino Espírito Santo Department of Gynecology and Obstetrics ]]></institution>
<addr-line><![CDATA[Ponta Delgada ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>30</day>
<month>06</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>30</day>
<month>06</month>
<year>2022</year>
</pub-date>
<volume>16</volume>
<numero>2</numero>
<fpage>166</fpage>
<lpage>170</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S1646-58302022000200166&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S1646-58302022000200166&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S1646-58302022000200166&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Herlyn-Werner-Wunderlich syndrome (HWW) is a rare congenital anomaly of the female urogenital tract, characterized by the triad of bicorporeal uterus, obstructed hemivagina and ipsilateral renal agenesis. The most common symptoms are pelvic pain, dysmenorrhea and an abdominal mass. Prompt surgical treatment is advisable. If not immediately possible, medical treatment should be initiated to induce amenorrhea. We describe a case of HWW with chronic pelvic pain and mild dysmenorrhea. The ultrasound revealed uterine duplication and a retro-uterine mass contiguous to the cervix. Magnetic resonance imaging (MRI) confirmed a genital tract anomaly. The patient was medicated with continuous oral estroprogestative and was proposed to surgery.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo O Síndrome de Herlyn-Werner-Wunderlich (HWW) é uma anomalia congénita rara do trato urogenital feminino, caraterizada pela tríade de útero bicorporal, hemivagina obstruída e agenesia renal ipsilateral. Os sintomas mais comuns são a dor pélvica, dismenorreia e presença de massa abdominal. É recomendado o tratamento cirúrgico atempado. No caso de impossibilidade, deve ser iniciado tratamento médico para indução da amenorreia. Descreve-se um caso de HWW em doente com dor pélvica crónica e dismenorreia ligeira. Ecograficamente constatada duplicação uterina e a presença de uma massa retro-uterina contigua ao colo uterino. A ressonância magnética confirmou a presença de malformação uterina. A doente foi medicada com estroprogestativo oral contínuo e proposta para cirurgia.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Uterine anomalies]]></kwd>
<kwd lng="en"><![CDATA[Dysmenorrhea]]></kwd>
<kwd lng="en"><![CDATA[Pelvic pain]]></kwd>
<kwd lng="en"><![CDATA[Unilateral renal agenesis]]></kwd>
<kwd lng="pt"><![CDATA[Anomalias uterinas]]></kwd>
<kwd lng="pt"><![CDATA[Dismenorreia]]></kwd>
<kwd lng="pt"><![CDATA[Dor pélvica]]></kwd>
<kwd lng="pt"><![CDATA[Agenesia renal unilateral]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Grimbizis]]></surname>
<given-names><![CDATA[GF]]></given-names>
</name>
<name>
<surname><![CDATA[Gordts]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[The ESHRE/ESGE consensus on the classification of female genital tract congenital anomalies Hum Reprod]]></article-title>
<collab>Di Spiezio Sardo A</collab>
<source><![CDATA[Aug]]></source>
<year>2013</year>
<volume>28</volume>
<numero>8</numero>
<issue>8</issue>
<page-range>2032-44</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Lee]]></surname>
<given-names><![CDATA[BH]]></given-names>
</name>
<name>
<surname><![CDATA[Kim]]></surname>
<given-names><![CDATA[JW]]></given-names>
</name>
<name>
<surname><![CDATA[Oh]]></surname>
<given-names><![CDATA[SI]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[3 Cases of Uterus Didelphys with an Obstructed Hemivagina and Ipsilateral Renal Agenesis]]></article-title>
<source><![CDATA[Korean J Obstet Gynecol]]></source>
<year>1997</year>
<volume>40</volume>
<numero>7</numero>
<issue>7</issue>
<page-range>1489-95</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Del Vescovo]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Battisti]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Di Paola]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Herlyn-Werner-Wunderlich syndrome MRI findings, radiological guide (two cases and literature review), and differential diagnosis. BMC Med Imaging]]></article-title>
<source><![CDATA[Mar 9]]></source>
<year>2012</year>
<volume>12</volume>
<page-range>4</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Zhu]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Chen]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Tong]]></surname>
<given-names><![CDATA[JL]]></given-names>
</name>
<name>
<surname><![CDATA[Wang]]></surname>
<given-names><![CDATA[W]]></given-names>
</name>
<name>
<surname><![CDATA[Zhang]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Lang]]></surname>
<given-names><![CDATA[JH]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[New classification of Herlyn-Werner-Wunderlich syndrome Chin Med J (Engl)]]></article-title>
<source><![CDATA[Jan 20]]></source>
<year>2015</year>
<volume>128</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>222-5</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Gholoum]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Puligandla]]></surname>
<given-names><![CDATA[PS]]></given-names>
</name>
<name>
<surname><![CDATA[Hui]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Su]]></surname>
<given-names><![CDATA[W]]></given-names>
</name>
<name>
<surname><![CDATA[Quiros]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Laberge]]></surname>
<given-names><![CDATA[JM]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Management and outcome of patients with combined vaginal septum, bifid uterus, and ipsilateral renal agenesis (Herlyn-Werner-Wunderlich syndrome) J Pediatr Surg]]></article-title>
<source><![CDATA[May]]></source>
<year>2006</year>
<volume>41</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>987-92</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Burgis]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Obstructive Müllerian anomalies case report, diagnosis, and management. Am J Obstet Gynecol]]></article-title>
<source><![CDATA[Aug]]></source>
<year>2001</year>
<volume>185</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>338-44</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Gruenwald]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[The relation of the growing müllerian duct to the wolffian duct and its importance for the genesis of malformations]]></article-title>
<source><![CDATA[Anat Rec]]></source>
<year>1941</year>
<volume>81</volume>
<page-range>1-20</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Hinckley]]></surname>
<given-names><![CDATA[MD]]></given-names>
</name>
<name>
<surname><![CDATA[Milki]]></surname>
<given-names><![CDATA[AA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Management of uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis A case report. J Reprod Med]]></article-title>
<source><![CDATA[Aug]]></source>
<year>2003</year>
<volume>48</volume>
<numero>8</numero>
<issue>8</issue>
<page-range>649-51</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Haddad]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Barranger]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Paniel]]></surname>
<given-names><![CDATA[BJ]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Blind hemivagina long-term follow-up and reproductive performance in 42 cases. Hum Reprod]]></article-title>
<source><![CDATA[Aug]]></source>
<year>1999</year>
<volume>14</volume>
<numero>8</numero>
<issue>8</issue>
<page-range>1962-4</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Prada Arias]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Muguerza Vellibre]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Montero Sánchez]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Vázquez Castelo]]></surname>
<given-names><![CDATA[JL]]></given-names>
</name>
<name>
<surname><![CDATA[Arias González]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Rodríguez Costa]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Uterus didelphys with obstructed hemivagina and multicystic dysplastic kidney Eur J Pediatr Surg]]></article-title>
<source><![CDATA[Dec]]></source>
<year>2005</year>
<volume>15</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>441-5</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Orazi]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Lucchetti]]></surname>
<given-names><![CDATA[MC]]></given-names>
</name>
<name>
<surname><![CDATA[Schingo]]></surname>
<given-names><![CDATA[PM]]></given-names>
</name>
<name>
<surname><![CDATA[Marchetti]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Ferro]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Herlyn-Werner-Wunderlich syndrome uterus didelphys, blind hemivagina and ipsilateral renal agenesis. Sonographic and MR findings in 11 cases. Pediatr Radiol]]></article-title>
<source><![CDATA[Jul]]></source>
<year>2007</year>
<volume>37</volume>
<numero>7</numero>
<issue>7</issue>
<page-range>657-65</page-range></nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Candiani]]></surname>
<given-names><![CDATA[GB]]></given-names>
</name>
<name>
<surname><![CDATA[Fedele]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Candiani]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Double uterus, blind hemivagina, and ipsilateral renal agenesis 36 cases and long-term follow-up. Obstet Gynecol]]></article-title>
<source><![CDATA[Jul]]></source>
<year>1997</year>
<volume>90</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>26-32</page-range></nlm-citation>
</ref>
<ref id="B13">
<label>13</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Tong]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Zhu]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Lang]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Clinical characteristics of 70 patients with Herlyn-Werner-Wunderlich syndrome Int J Gynaecol Obstet]]></article-title>
<source><![CDATA[May]]></source>
<year>2013</year>
<volume>121</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>173-5</page-range></nlm-citation>
</ref>
<ref id="B14">
<label>14</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Güdücü]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Gönenç]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Isçi]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Yigiter]]></surname>
<given-names><![CDATA[AB]]></given-names>
</name>
<name>
<surname><![CDATA[Dünder]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Herlyn-Werner-Wunderlich syndrome-timely diagnosis is important to preserve fertility J Pediatr Adolesc Gynecol]]></article-title>
<source><![CDATA[Oct]]></source>
<year>2012</year>
<volume>25</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>e111-2</page-range></nlm-citation>
</ref>
<ref id="B15">
<label>15</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Sanghvi]]></surname>
<given-names><![CDATA[Y]]></given-names>
</name>
<name>
<surname><![CDATA[Shastri]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Mane]]></surname>
<given-names><![CDATA[SB]]></given-names>
</name>
<name>
<surname><![CDATA[Dhende]]></surname>
<given-names><![CDATA[NP]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Prepubertal presentation of Herlyn-Werner-Wunderlich syndrome a case report. J Pediatr Surg]]></article-title>
<source><![CDATA[Jun]]></source>
<year>2011</year>
<volume>46</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>1277-80</page-range></nlm-citation>
</ref>
<ref id="B16">
<label>16</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Pansini]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Torricelli]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Gomarasca]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Brambilla]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Beolchi]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Sideri]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Acute urinary retention due to didelphys uterus associated with an obstructed hemivagina in a 5-month-old infant J Pediatr Surg]]></article-title>
<source><![CDATA[Oct]]></source>
<year>1988</year>
<volume>23</volume>
<numero>10</numero>
<issue>10</issue>
<page-range>984-5</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
