<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2183-1351</journal-id>
<journal-title><![CDATA[Acta Radiológica Portuguesa]]></journal-title>
<abbrev-journal-title><![CDATA[Acta Radiol Port]]></abbrev-journal-title>
<issn>2183-1351</issn>
<publisher>
<publisher-name><![CDATA[Sociedade Portuguesa de Radiologia e Medicina Nuclear]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2183-13512022000200039</article-id>
<article-id pub-id-type="doi">10.25748/arp.25330</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Left Isomerism - Magnetic Resonance Diagnosis]]></article-title>
<article-title xml:lang="pt"><![CDATA[Síndrome Heterotáxica com Poliesplenia - Diagnóstico Tomográfico]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Silva]]></surname>
<given-names><![CDATA[Mayara Oliveira da]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Abreu]]></surname>
<given-names><![CDATA[Bruno Fernandes Barros Brehme de]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Duarte]]></surname>
<given-names><![CDATA[Márcio Luís]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Clinica Mega Imagem  ]]></institution>
<addr-line><![CDATA[São Paulo ]]></addr-line>
<country>Brasil</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,WEBIMAGEM Telerradiologia  ]]></institution>
<addr-line><![CDATA[São Paulo ]]></addr-line>
<country>Brasil</country>
</aff>
<pub-date pub-type="pub">
<day>30</day>
<month>08</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>30</day>
<month>08</month>
<year>2022</year>
</pub-date>
<volume>34</volume>
<numero>2</numero>
<fpage>39</fpage>
<lpage>42</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S2183-13512022000200039&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S2183-13512022000200039&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S2183-13512022000200039&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Heterotaxy syndrome is a rare congenital condition with multifactorial inheritance in which the internal organs are abnormally arranged in the chest and abdomen. It can be classified into two main subcategories: heterotaxy syndrome with polysplenia (left isomerism) and heterotaxy syndrome with asplenia (right isomerism). Such a distinction between these subcategories offers better means of indicating the genetic alterations responsible for the syndrome. Individuals with this condition have complex congenital abnormalities, affecting various organs such as the heart - interferes in blood transport - and lung - altering the number of pulmonary lobes. We report a case of heterotaxy syndrome with polysplenia without abnormality in the thoracic organs in an adult patient.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo A síndrome heterotáxica é uma condição congênita rara com herança multifatorial em que os órgãos internos estão arranjados anormalmente no tórax e abdome, podendo ser classificadas em duas subcategorias principais: síndrome heterotáxica com poliesplenia (isomerismo esquerdo) e síndrome heterotáxica com asplenia (isomerismo direito). Indivíduos com esta condição têm complexas anormalidades congênitas acometendo diversos órgãos, como o coração - dificultando o transporte sanguíneo - e o pulmão - alterando o número de lobos. Relatamos um caso de síndrome heterotáxica com poliesplenia sem anormalidade nos órgãos torácicos em paciente adulta.]]></p></abstract>
<kwd-group>
<kwd lng="pt"><![CDATA[Síndrome heterotáxica]]></kwd>
<kwd lng="pt"><![CDATA[Poliesplenia]]></kwd>
<kwd lng="pt"><![CDATA[Agenesia do corpo e cauda do pâncreas]]></kwd>
<kwd lng="pt"><![CDATA[Ressonância Magnética]]></kwd>
<kwd lng="pt"><![CDATA[Diagnóstico.]]></kwd>
<kwd lng="en"><![CDATA[Heterotaxic syndrome]]></kwd>
<kwd lng="en"><![CDATA[Polysplenia]]></kwd>
<kwd lng="en"><![CDATA[Agenesis of the body and tail of the pancreas]]></kwd>
<kwd lng="en"><![CDATA[Magnetic resonance imaging]]></kwd>
<kwd lng="en"><![CDATA[Diagnosis.]]></kwd>
</kwd-group>
</article-meta>
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