<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2184-0628</journal-id>
<journal-title><![CDATA[Gazeta Médica]]></journal-title>
<abbrev-journal-title><![CDATA[Gaz Med]]></abbrev-journal-title>
<issn>2184-0628</issn>
<publisher>
<publisher-name><![CDATA[Círculo Médico]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2184-06282024000400326</article-id>
<article-id pub-id-type="doi">10.29315/gm.v11i4.810</article-id>
<title-group>
<article-title xml:lang="pt"><![CDATA[Síndrome de Ramsay-Hunt com Polineuropatia Craniana e Disfagia Grave: Uma Entidade Rara e Multidisciplinar]]></article-title>
<article-title xml:lang="en"><![CDATA[Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rocha]]></surname>
<given-names><![CDATA[Gustavo Pedrosa]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Soares]]></surname>
<given-names><![CDATA[Mafalda Trindade]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Delgado]]></surname>
<given-names><![CDATA[Sofia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Saraiva]]></surname>
<given-names><![CDATA[Marlene]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Matos]]></surname>
<given-names><![CDATA[Catarina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Freire]]></surname>
<given-names><![CDATA[Filipe]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Prof. Doutor Fernando da Fonseca Serviço de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço ]]></institution>
<addr-line><![CDATA[Amadora ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Prof. Doutor Fernando da Fonseca Serviço de Neurologia ]]></institution>
<addr-line><![CDATA[Amadora ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital Prof. Doutor Fernando da Fonseca Serviço de Medicina Física e Reabilitação ]]></institution>
<addr-line><![CDATA[Amadora ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2024</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2024</year>
</pub-date>
<volume>11</volume>
<numero>4</numero>
<fpage>326</fpage>
<lpage>330</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S2184-06282024000400326&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S2184-06282024000400326&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S2184-06282024000400326&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo A síndrome de Ramsay-Hunt (SRH) caracteriza-se como uma infeção do gânglio geniculado do nervo facial pelo vírus varicella zoster (VVZ) e apresenta-se pela tríada de otalgia, erupção vesicular da concha auricular e paralisia facial periférica ipsilateral. O envolvimento de outros pares cranianos é raro, mas pode trazer dificuldade e atraso diagnóstico e um mau prognóstico. Apresentamos o caso de um doente com SRH e extensão a polineuropatia afetando o V, VII, VIII, IX e X pares cranianos e consequente sintomatologia que motivou internamento hospitalar prolongado e uma abordagem multidisciplinar de diferentes especialidades médicas. Apesar do mau prognóstico, apresentou uma significativa recuperação clínica e radiológica. A prevenção e a atenuação do VVZ e das suas complicações são cada vez mais possíveis e o aumento do conhecimento sobre a doença para a população e para os clínicos poderá ter impacto significativo.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Ramsay-Hunt syndrome is defined by varicella-zoster virus (VZV) reactivation in the geniculate ganglion of the facial nerve and its presentation involves otalgia, vesicular lesions of the outer ear and ipsilateral facial paralysis. Cranial polyneuropathy extension is rare, can sometimes take a challenging and delayed diagnosis and poor prognosis. We illustrate a case of varicella zoster virus cranial polyneuropathy affecting V, VII, VIII, IX and X cranial nerves and consequent symptomatology that led to prolonged hospitalization with multidisciplinary approach. Despite the poor prognosis, the patient had a significant clinical and imagiological improvement. Prevention and attenuation of VZV and its complications are becoming increasingly possible and the increase in knowledge about this disease for the population and physicians can have a significant impact.]]></p></abstract>
<kwd-group>
<kwd lng="pt"><![CDATA[Doenças dos Nervos Cranianos]]></kwd>
<kwd lng="pt"><![CDATA[Herpes Zoster Oticus]]></kwd>
<kwd lng="pt"><![CDATA[Nervos Cranianos]]></kwd>
<kwd lng="pt"><![CDATA[Paralisia Facial]]></kwd>
<kwd lng="en"><![CDATA[Cranial Nerve Diseases]]></kwd>
<kwd lng="en"><![CDATA[Cranial Nerves]]></kwd>
<kwd lng="en"><![CDATA[Facial Paralysis]]></kwd>
<kwd lng="en"><![CDATA[Herpes Zoster Oticus]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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