<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2184-6499</journal-id>
<journal-title><![CDATA[Revista Portuguesa Otorrinolaringologia e Cirurgia de Cabeça e Pescoço]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Port ORL]]></abbrev-journal-title>
<issn>2184-6499</issn>
<publisher>
<publisher-name><![CDATA[Sociedade Portuguesa de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2184-64992022000400371</article-id>
<article-id pub-id-type="doi">10.34631/sporl.1059</article-id>
<title-group>
<article-title xml:lang="pt"><![CDATA[O papel da Amigdalectomia na Síndrome de PFAPA: Revisão da literatura e estudo retrospetivo]]></article-title>
<article-title xml:lang="en"><![CDATA[Role of Tonsillectomy in PFAPA Syndrome: A Literature Review and Retrospective Study]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Gomes]]></surname>
<given-names><![CDATA[Pedro Marques]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Costa]]></surname>
<given-names><![CDATA[Sílvia Duarte]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Gonçalves]]></surname>
<given-names><![CDATA[Ana Isabel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Azevedo]]></surname>
<given-names><![CDATA[Paula]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Duarte]]></surname>
<given-names><![CDATA[Delfim]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Pedro Hispano Unidade Local de Saúde de Matosinhos ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<volume>60</volume>
<numero>4</numero>
<fpage>371</fpage>
<lpage>376</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S2184-64992022000400371&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S2184-64992022000400371&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S2184-64992022000400371&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo  Objetivo: Revisão da literatura e comparar a efetividade da terapêutica farmacológica com a amigdalectomia na remissão da doença.  Material e métodos: Análise retrospetiva dos dados clínicos (idade, género, clínica, antecedentes familiares) tipos de tratamento efetuado (médico e/ou cirúrgico), tempo de remissão (após tratamento médico e cirúrgico) e a remissão no 1º, 3º e 6º mês após amigdalectomia em crianças com síndrome de PFAPA avaliadas no Hospital Pedro Hispano entre janeiro de 2016 e dezembro de 2021.  Resultados:  Foram avaliadas 9 crianças (56 % do sexo feminino, 44 % do sexo masculino) com idades que variaram entre 1 e 4 anos (idade média 1,9 ± 1,3 anos). Ao diagnóstico o número médio de semanas de remissão foi de 4,0 ± 1,8. Após corticoterapia foi de 3,88 ± 1,0 e após amigdalectomia de 50,6 ± 33,8 semanas.  Conclusão: A amigdalectomia demonstrou ser uma opção terapêutica muito útil na remissão da doença em crianças com síndrome de PFAPA.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Objective:  Literature review and compare the pharmacological therapeutics effectiveness with the tonsillectomy in the disease remission.  Material and methods: Retrospective analysis of clinical data (age, gender, clinic, family history), types of treatment (pharmacological and/or surgical), time of remission (after medical and surgical treatment) and remission in the 1st, 3rd and 6th month after tonsillectomy in children with PFAPA syndrome evaluated at Hospital Pedro Hispano between January 2016 and December 2021.  Results:  Nine children were evaluated (56% female, 44% male) aged between 1 and 4 years old (mean age 1.9 ± 1.3 years). At diagnosis, the mean number of weeks of remission was 4.0 ± 1.8. After corticotherapy it was 3.88 ± 1.0 and after tonsillectomy it was 50.6 ± 33.8 weeks.  Conclusion: Tonsillectomy has demonstrated to be a very useful therapeutic option in the disease&#8217;s remission in children with PFAPA syndrome.]]></p></abstract>
<kwd-group>
<kwd lng="pt"><![CDATA[Síndrome de PFAPA]]></kwd>
<kwd lng="pt"><![CDATA[Amigdalectomia]]></kwd>
<kwd lng="pt"><![CDATA[Corticoterapia]]></kwd>
<kwd lng="pt"><![CDATA[Colchicina]]></kwd>
<kwd lng="en"><![CDATA[PFAPA Syndrome]]></kwd>
<kwd lng="en"><![CDATA[Tonsillectomy]]></kwd>
<kwd lng="en"><![CDATA[Corticotherapy]]></kwd>
<kwd lng="en"><![CDATA[Colchicine]]></kwd>
</kwd-group>
</article-meta>
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