<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2184-6499</journal-id>
<journal-title><![CDATA[Revista Portuguesa Otorrinolaringologia e Cirurgia de Cabeça e Pescoço]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Port ORL]]></abbrev-journal-title>
<issn>2184-6499</issn>
<publisher>
<publisher-name><![CDATA[Sociedade Portuguesa de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2184-64992025000300339</article-id>
<article-id pub-id-type="doi">10.34631/sporl.3133</article-id>
<title-group>
<article-title xml:lang="pt"><![CDATA[Displasia isolada da apófise longa da bigorna - um caso clínico]]></article-title>
<article-title xml:lang="en"><![CDATA[Incus long process dysplasia - a clinical case]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cunha]]></surname>
<given-names><![CDATA[António Trigueiros]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cunha]]></surname>
<given-names><![CDATA[Nuno Trigueiros]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Duarte]]></surname>
<given-names><![CDATA[Constança Oom]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Fernandes]]></surname>
<given-names><![CDATA[João Rainha]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Machado]]></surname>
<given-names><![CDATA[Maria Pimenta]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Macor]]></surname>
<given-names><![CDATA[Carlos]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Beatriz Ângelo, Loures  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital CUF Trindade  ]]></institution>
<addr-line><![CDATA[Porto ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>09</month>
<year>2025</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>09</month>
<year>2025</year>
</pub-date>
<volume>63</volume>
<numero>3</numero>
<fpage>339</fpage>
<lpage>343</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S2184-64992025000300339&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S2184-64992025000300339&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S2184-64992025000300339&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo As malformações do ouvido médio são eventos raros, ocorrendo em 1/15000 nados vivos1-3. Estão geralmente associadas a outras malformações da cabeça e do pescoço podendo também ser parte integrante de síndromes malformativas. As malformações isoladas do ouvido médio são, por isso, eventos ainda mais raros cujo diagnóstico é desafiante4, sendo dificultado pela normal aparência do pavilhão auricular, canal auditivo externo e membrana timpânica. Neste artigo, iremos descrever um caso clínico de uma doente de 19 anos com história de surdez unilateral não tratada desde a infância. Ao exame objetivo ORL não apresentava alterações, tendo sido pedidos exames audiométricos que demonstraram uma surdez de condução no ouvido esquerdo com um gap aéro-ósseo de 54dB com timpanograma tipo A. O relatório da TC não descrevia alterações pelo que foi proposta uma timpanotomia exploradora que revelou uma displasia isolada da longa apófise da bigorna. Foi realizada uma ossiculoplastia do tipo II (classificação de Portmann)14 com enxerto autólogo de cortical mastoideia e cartilagem do tragus. O audiograma pós-operatório demonstrou uma redução do GAO médio para 18.75dB.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Middle ear malformations are rare events, occurring in approximately 1 in 15,000 live births.1-3 They are generally associated with other head and neck anomalies and may also be part of syndromic malformations. Isolated malformations of the middle ear are therefore even rarer and pose a diagnostic challenge4, especially given the normal appearance of the auricle, external auditory canal, and tympanic membrane. In this article, we describe the clinical case of a 19-year-old female patient with a history of untreated hearing loss since childhood. Otolaryngological examination revealed no abnormalities, prompting further audiometric evaluation. Pure tone audiometry demonstrated a left-sided conductive hearing loss with an air-bone gap (ABG) of 54 dB and a type A tympanogram. Computed tomography (CT) was reported as normal. An exploratory tympanotomy was therefore performed, revealing an isolated dysplasia of the long process of the incus. A type II ossiculoplasty (Portmann classification)14 was performed using autologous cortical mastoid bone and tragal cartilage grafts. The postoperative audiogram showed a reduction in the average ABG to 18.75 dB.]]></p></abstract>
<kwd-group>
<kwd lng="pt"><![CDATA[Displasia]]></kwd>
<kwd lng="pt"><![CDATA[Bigorna]]></kwd>
<kwd lng="pt"><![CDATA[Malformação]]></kwd>
<kwd lng="en"><![CDATA[Dysplasia]]></kwd>
<kwd lng="en"><![CDATA[Incus]]></kwd>
<kwd lng="en"><![CDATA[Malformation]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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