<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2341-4545</journal-id>
<journal-title><![CDATA[GE-Portuguese Journal of Gastroenterology]]></journal-title>
<abbrev-journal-title><![CDATA[GE Port J Gastroenterol]]></abbrev-journal-title>
<issn>2341-4545</issn>
<publisher>
<publisher-name><![CDATA[Sociedade Portuguesa de Gastrenterologia]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2341-45452023000300066</article-id>
<article-id pub-id-type="doi">10.1159/000521518</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[A Rare Case of Ectopic Adrenocorticotropic Hormone Secretion from Pancreatic Neuroendocrine Tumour Presenting with Cushing Syndrome]]></article-title>
<article-title xml:lang="pt"><![CDATA[Um caso raro de secreção ectópica de hormona adrenocorticotrópica por tumor neuroendócrino pancreático apresentando-se com síndroma de Cushing]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Lee]]></surname>
<given-names><![CDATA[Soon Liang]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ng]]></surname>
<given-names><![CDATA[Chiun Yann]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sidhu]]></surname>
<given-names><![CDATA[Jasminder]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Awang]]></surname>
<given-names><![CDATA[Asmawiza]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Kuala Lumpur General Hospital, Ministry of Health Department of Medicine Gastroenterology and Hepatology Unit]]></institution>
<addr-line><![CDATA[Kuala Lumpur ]]></addr-line>
<country>Malaysia</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Ministry of Health Kuala Lumpur General Hospital Department of Pathology]]></institution>
<addr-line><![CDATA[Kuala Lumpur ]]></addr-line>
<country>Malaysia</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>06</month>
<year>2023</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>06</month>
<year>2023</year>
</pub-date>
<volume>30</volume>
<numero>3</numero>
<fpage>66</fpage>
<lpage>69</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S2341-45452023000300066&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S2341-45452023000300066&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S2341-45452023000300066&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Ectopic adrenocorticotropic hormone secretion (EAS) from the pancreatic neuroendocrine tumour (PNET) is rare, aggressive, and challenging to treat. We hereby present a rare case of EAS from PNET presenting with Cushing syndrome diagnosed with endoscopic ultrasound-guided fine-needle aspiration cytology. This case highlights the advanced presentation of EAS from PNET with poor clinical correlation of hypercortisolism and the grade of PNET.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo A secreção ectópica de hormona adrenocorticotrópica (SEA) por tumores neuroendócrinos pancreáticos (TNE-P) é rara, agressiva e difícil de tratar. Apresentamos um caso raro de SEA por TNE-P apresentando-se com síndroma de Cushing, diagnosticado através de ecoendoscopia com punção aspirativa com agulha fina. Este caso enfatiza a apresentação avançada dos TNE-P com SEA e a correlação baixa com o grau de hipercortisolismo e o grau do TNE-P.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Adrenocorticotropic hormone]]></kwd>
<kwd lng="en"><![CDATA[Pancreatic neuroendocrine tumour]]></kwd>
<kwd lng="en"><![CDATA[Cushing syndrome]]></kwd>
<kwd lng="pt"><![CDATA[Hormona adrenocorticotrópica]]></kwd>
<kwd lng="pt"><![CDATA[Tumor neuroendócrino pancreático]]></kwd>
<kwd lng="pt"><![CDATA[Síndroma de Cushing]]></kwd>
</kwd-group>
</article-meta>
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