<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2341-4545</journal-id>
<journal-title><![CDATA[GE-Portuguese Journal of Gastroenterology]]></journal-title>
<abbrev-journal-title><![CDATA[GE Port J Gastroenterol]]></abbrev-journal-title>
<issn>2341-4545</issn>
<publisher>
<publisher-name><![CDATA[Sociedade Portuguesa de Gastrenterologia]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2341-45452023000600028</article-id>
<article-id pub-id-type="doi">10.1159/000527209</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Endoscopic Approach to Duodenal Adenomas in Familial Adenomatous Polyposis: A Retrospective Cohort]]></article-title>
<article-title xml:lang="pt"><![CDATA[Abordagem endoscópica de adenomas duodenais na Polipose Adenomatosa Familiar: um coorte retrospetivo]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Garcia]]></surname>
<given-names><![CDATA[Joana Lemos]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rosa]]></surname>
<given-names><![CDATA[Isadora]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Silva]]></surname>
<given-names><![CDATA[João Pereira da]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Lage]]></surname>
<given-names><![CDATA[Pedro]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Claro]]></surname>
<given-names><![CDATA[Isabel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Português de Oncologia de Lisboa Francisco Gentil E.P.E. Gastroenterology Department ]]></institution>
<addr-line><![CDATA[Lisboa ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Instituto Português de Oncologia de Lisboa Francisco Gentil E.P.E. Familial Risk Clinic ]]></institution>
<addr-line><![CDATA[Lisboa ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>30</day>
<month>12</month>
<year>2023</year>
</pub-date>
<pub-date pub-type="epub">
<day>30</day>
<month>12</month>
<year>2023</year>
</pub-date>
<volume>30</volume>
<numero>6</numero>
<fpage>28</fpage>
<lpage>34</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S2341-45452023000600028&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S2341-45452023000600028&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S2341-45452023000600028&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Introduction:  Over 90% of the patients with familial adenomatous polyposis (FAP) will develop duodenal adenomas.  Aim:  The aim of this study was to evaluate the effectiveness and safety of endoscopic excision of large duodenal adenomas in FAP patients.  Methods:  All FAP patients from a familial risk clinic submitted to endoscopic therapy for duodenal adenomas &#8805;10 mm between January 2010 and February 2021 were included.  Results:  From 151 FAP families, 22 patients (50 lesions) were included: 54.5% female; median follow-up 8.5 (IQR: 5.8-12.3) years after the first endoscopy. First therapeutic endoscopy occurred at a median age of 41.0 years (IQR: 33.0-58.2). Repeat therapeutic endoscopy was required in 54.5% of patients. Median size of the largest adenoma was 15 mm (IQR: 10-18 mm); resection was piece-meal in 63.1% and en bloc in the remaining. In 2 cases, the resection was incomplete (fibrosis due to previous resection and difficult positioning). Complications occurred in 6.3% of the resected lesions (4 patients): 2 immediate (bleeding, perforation); 4 in the first week (1 bleeding, 2 mild pancreatitis, 1 perforation requiring surgery; the latter two after ampullectomy). Histology revealed low-grade dysplasia adenomas in 90.1%; no adenocarcinomas were found. One patient with Spigelman stage IV disease not amenable to endoscopic control underwent elective duodenopancreatectomy (without duodenal cancer).  Conclusion:  Endoscopic surveillance and treatment of duodenal adenomas in FAP patients was safe and effective in the prevention of duodenal cancer.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo  Introdução:  Mais de 90% dos doentes com Polipose Adenomatosa Familiar (PAF) desenvolvem adenomas duodenais.  Objetivo:  Avaliar a eficácia e segurança da excisão endoscópica de adenomas duodenais em doentes com PAF.  Métodos:  Incluídos todos os doentes com PAF submetidos a terapêutica endoscópica de adenomas duodenais &#8805;10 mm entre janeiro/2010-fevereiro/2021.  Resultados:  Em 151 famílias com PAF, incluídos 22 doentes (50 lesões): 54.5% mulheres; mediana do follow-up 12.3 (IQR: 6.0-19.0) anos. Primeira endoscopia terapêutica (resseção de pólipos duodenais &#8805;10 mm) ocorreu numa mediana de idades 41.0 (IQR: 33.0-58.2) anos.Em 54.5% dos casos, foi necessária uma nova endoscopia terapêutica. Dimensão mediana do maior adenoma: 15 mm (IQR: 10-18 mm); resseção realizada em piecemeal em 63.1% e em bloco nos restantes. Em dois casos, a resseção endoscópica foi incompleta (fibrose em local de resseção prévia:1; posicionamento:1). Complicações em 6.3% das lesões ressecadas (4 doentes): 2 imediatas (hemorragia e perfuração, manejadas endoscopicamente); 4 na primeira semana (1 hemorragia controlada endoscopicamente, 2 pancreatites ligeiras tratadas conservadoramente, 1 perfuração com necessidade de cirurgia; as duas últimas após ampulectomia). A avaliação histológica revelou adenomas com displasia de baixo grau em 90.1%; nenhum adenocarcinoma. Um doente com doença Spigelman IV não controlável endoscopicamente realizou duodenopancreatectomia (sem cancro).  Conclusão:  A vigilância e tratamento endoscópicos de adenomas duodenais em doentes com PAF revelaram-se seguros e eficazes na prevenção de cancro duodenal.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Familial adenomatous polyposis]]></kwd>
<kwd lng="en"><![CDATA[Duodenum]]></kwd>
<kwd lng="en"><![CDATA[Adenomas]]></kwd>
<kwd lng="en"><![CDATA[Endoscopy]]></kwd>
<kwd lng="en"><![CDATA[Endoscopic mucosal resection]]></kwd>
<kwd lng="pt"><![CDATA[Polipose adenomatosa familiar]]></kwd>
<kwd lng="pt"><![CDATA[Duodeno]]></kwd>
<kwd lng="pt"><![CDATA[Adenomas]]></kwd>
<kwd lng="pt"><![CDATA[Endoscopia]]></kwd>
<kwd lng="pt"><![CDATA[Mucosectomia]]></kwd>
</kwd-group>
</article-meta>
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