<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2795-5001</journal-id>
<journal-title><![CDATA[Portuguese Journal of Dermatology and Venereology]]></journal-title>
<abbrev-journal-title><![CDATA[Port J Dermatol Venereol.]]></abbrev-journal-title>
<issn>2795-5001</issn>
<publisher>
<publisher-name><![CDATA[Permanyer Publications]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2795-50012024000200122</article-id>
<article-id pub-id-type="doi">10.24875/pjdv.23000104</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Hutchinson&#8217;s sign in congenital nail matrix nevus]]></article-title>
<article-title xml:lang="pt"><![CDATA[Sinal de Hutchinson no nevo congénito da matriz ungueal]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ferreirinha]]></surname>
<given-names><![CDATA[Ana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Fialho]]></surname>
<given-names><![CDATA[Maria C.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Garrido]]></surname>
<given-names><![CDATA[Pedro M.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Costa-Rosa]]></surname>
<given-names><![CDATA[Joaninha]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Moura]]></surname>
<given-names><![CDATA[Cecília]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Centro Hospitalar Universitário de Lisboa Central Hospital de Santo António dos Capuchos Department of Dermatology and Venereology]]></institution>
<addr-line><![CDATA[Lisbon ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Instituto Português de Oncologia de Lisboa Department of Dermatology and Venereology ]]></institution>
<addr-line><![CDATA[Lisbon ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Instituto Português de Oncologia de Lisboa Department of Anatomic Pathology ]]></institution>
<addr-line><![CDATA[Lisbon ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>30</day>
<month>06</month>
<year>2024</year>
</pub-date>
<pub-date pub-type="epub">
<day>30</day>
<month>06</month>
<year>2024</year>
</pub-date>
<volume>82</volume>
<numero>2</numero>
<fpage>122</fpage>
<lpage>125</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S2795-50012024000200122&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S2795-50012024000200122&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S2795-50012024000200122&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Congenital nail matrix nevi (NMN) are a rare cause of melanonychia that may present with irregularity, asymmetry, and multicomponent pigmentation posing diagnostic challenges with subungual melanoma. We report a case of a 49-year-old female with longitudinal melanonychia and a 1-month recent pigmentation in the proximal nail fold. This sign is traditionally associated with malignancy, which further complicates the differentiation from acral melanoma. Therefore, a nail matrix biopsy was performed. Histopathologic examination revealed a nail matrix nevus. This procedure is crucial in suspicious cases, despite the risk of nail dystrophia. The evolution of these nevi into adulthood and their potential malignancy remains unclear, emphasizing the need for continued research and surveillance. This case highlights that congenital NMN often present with clinical and dermoscopic features of concern, mirroring those observed in subungual melanoma.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo Os nevos congénitos da matriz ungueal são uma causa rara de melanoníquia que pode apresentar-se com irregularidade, assimetria e pigmentação multicomponente, o que dificulta o diagnóstico diferencial com melanoma subungueal. Descrevemos o caso de uma mulher de 49 anos com melanoníquia longitudinal que progrediu com pigmentação na prega ungueal proximal. O sinal de Hutchinson está frequentemente associado a malignidade, o que dificulta ainda mais a diferenciação com o melanoma acral. Realizou-se uma biópsia da matriz ungueal, cujo exame histopatológico foi compatível com nevo da matriz ungueal. Esta abordagem é crucial em casos suspeitos, apesar do risco de distrofia ungueal. A evolução destes nevos até à idade adulta e o seu potencial de malignidade permanecem pouco claros, enfatizando a necessidade de vigilância contínua. Este caso realça que os nevos congénitos da matriz ungueal se apresentam frequentemente com características clínicas e dermatoscópicas suspeitas, que podem mimetizar as observadas no melanoma subungueal.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Congenital melanocytic nevus]]></kwd>
<kwd lng="en"><![CDATA[Congenital nail matrix nevus]]></kwd>
<kwd lng="en"><![CDATA[Dermoscopy]]></kwd>
<kwd lng="en"><![CDATA[Hutchinson&#8217;s sign]]></kwd>
<kwd lng="en"><![CDATA[Longitudinal melanonychia]]></kwd>
<kwd lng="en"><![CDATA[Subungual melanoma]]></kwd>
<kwd lng="pt"><![CDATA[Dermatoscopia]]></kwd>
<kwd lng="pt"><![CDATA[Melanoma subungueal]]></kwd>
<kwd lng="pt"><![CDATA[Melanoníquia longitudinal]]></kwd>
<kwd lng="pt"><![CDATA[Nevo melanocítico congénito]]></kwd>
<kwd lng="pt"><![CDATA[Nevo congénito da matriz da unha]]></kwd>
<kwd lng="pt"><![CDATA[Sinal de Hutchinson]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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