<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2795-5001</journal-id>
<journal-title><![CDATA[Portuguese Journal of Dermatology and Venereology]]></journal-title>
<abbrev-journal-title><![CDATA[Port J Dermatol Venereol.]]></abbrev-journal-title>
<issn>2795-5001</issn>
<publisher>
<publisher-name><![CDATA[Permanyer Publications]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2795-50012026000100046</article-id>
<article-id pub-id-type="doi">10.24875/pjdv.25000049</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Desmoplastic trichoepithelioma on the face mimicking basal cell carcinoma: a case report and literature review]]></article-title>
<article-title xml:lang="pt"><![CDATA[Tricoepitelioma desmoplásico na face simulando carcinoma basocelular: um relato de caso e revisão da literatura]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Saldanha]]></surname>
<given-names><![CDATA[Isabele M.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Motizuki]]></surname>
<given-names><![CDATA[Airton K.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Oyama-Okajima]]></surname>
<given-names><![CDATA[Renata M.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,João de Barros Barreto University Hospital Dermatology Service of the Federal University of Pará ]]></institution>
<addr-line><![CDATA[Belém ]]></addr-line>
<country>Brazil</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Faculty of Medicine of Federal University of Pará Department of Medicine ]]></institution>
<addr-line><![CDATA[Belém ]]></addr-line>
<country>Brazil</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2026</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2026</year>
</pub-date>
<volume>84</volume>
<numero>1</numero>
<fpage>46</fpage>
<lpage>49</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_arttext&amp;pid=S2795-50012026000100046&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_abstract&amp;pid=S2795-50012026000100046&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.pt/scielo.php?script=sci_pdf&amp;pid=S2795-50012026000100046&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Desmoplastic trichoepithelioma is a rare benign cutaneous neoplasm that differentiates toward germinative cells of the hair follicle. It can be classified as familial multiple trichoepithelioma, solitary, and desmoplastic, the latter being a rare variant with low incidence and clinical features resembling basal cell carcinoma. We report the case of a 54-year-old female patient who presented with a brownish plaque exhibiting areas of dark pigmentation, an irregular outline, a pearly sheen, and surface telangiectasias in the right paranasal region. Complementary studies, including histopathological and immunohistochemical analyses, were performed to establish the definitive diagnosis. Furthermore, this cutaneous lesion displays both clinical and histopathological characteristics that complicate differentiation between benign and malignant tumors, making immunohistochemistry essential to confirm the desmoplastic variant of trichoepithelioma.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo O tricoepitelioma desmoplásico é uma rara neoplasia benigna de pele que se diferencia em células germinativas do folículo piloso, e pode ser classificado entre tricoepitelioma múltiplo familial, solitário e desmoplásico, sendo esse último uma variante rara com pouca incidência na população e com similaridades clínicas do carcinoma basocelular. O caso é de uma paciente de 54 anos,que apresentou uma placa acastanhada, com algumas áreas de pigmentos enegrecidos, irregular, com brilho perláceo e telangiectasias em sua superfície na região paranasal direita, sendo realizado exames complementares como o anatopatológico e imunohistoquímico para confirmação completa do diagnóstico. Além disso, essa lesão no tegumento manifesta estruturas tanto clínicas quanto histopatológicas que dificultam na diferenciação de tumores malignos ou benignos, sendo fundamental a realização da imunohistoquímica para confirmar essa variante desmoplásica do tricoepitelioma.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Desmoplastic trichoepithelioma]]></kwd>
<kwd lng="en"><![CDATA[Differential diagnosis]]></kwd>
<kwd lng="en"><![CDATA[Basal cell carcinoma]]></kwd>
<kwd lng="pt"><![CDATA[Tricoepitelioma desmoplásico]]></kwd>
<kwd lng="pt"><![CDATA[Diagnóstico diferencial]]></kwd>
<kwd lng="pt"><![CDATA[Carcinoma basocelular]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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